ICD-10 Coding for Alpha-1 Antitrypsin Deficiency(E88.01)
Complete ICD-10-CM coding and documentation guide for Alpha-1 Antitrypsin Deficiency. Includes clinical validation requirements, documentation requirements, and coding pitfalls.
Also known as:
Related ICD-10 Code Ranges
Complete code families applicable to Alpha-1 Antitrypsin Deficiency
E88.0-E88.9Primary Range
Metabolic disorders
This range includes codes for metabolic disorders, with E88.01 specifically for alpha-1 antitrypsin deficiency.
Key Information: ICD-10 code for alpha-1 antitrypsin deficiency
Essential facts and insights about Alpha-1 Antitrypsin Deficiency
Primary ICD-10-CM Code for alpha 1 antitrypsin deficiency
Decision Criteria
clinical Criteria
- Serum AAT level <80 mg/dL
documentation Criteria
- Phenotype PiZZ, PiSZ, or PiNull documented
Applicable To
- Genetic deficiency of alpha-1-antitrypsin
Clinical Validation Requirements
- Serum AAT level <80 mg/dL
- Phenotype PiZZ, PiSZ, or PiNull
- Liver biopsy showing PAS-positive globules
Code-Specific Risks
- Incorrect sequencing with related conditions
- Missing phenotype documentation
Coding Notes
- Ensure phenotype and serum levels are documented to support the use of E88.01.
Ancillary Codes
Additional codes that should be used in conjunction with the main diagnosis codes when applicable.
Documentation & Coding Risks
Avoid these common documentation and coding issues when documenting Alpha-1 Antitrypsin Deficiency to ensure proper reimbursement, maintain compliance, and reduce audit risk. These guidelines are particularly important when using ICD-10 code E88.01.
Impact
Clinical: Leads to misdiagnosis or underdiagnosis., Regulatory: Non-compliance with documentation standards., Financial: Potential claim denials due to insufficient documentation.
Mitigation Strategy
Include specific lab results and phenotype in documentation., Use structured templates for documentation.
Impact
Reimbursement: Incorrect sequencing can lead to claim denials., Compliance: Non-compliance with coding guidelines., Data Quality: Inaccurate representation of patient's condition.
Mitigation Strategy
Sequence E88.01 first with J43.9 as secondary.
Impact
Lack of phenotype documentation can lead to audit findings.
Mitigation Strategy
Ensure phenotype is documented in all cases of AATD.
Documentation errors, coding pitfalls, and audit risks are interconnected aspects of medical coding and billing. Addressing all three areas helps ensure accurate coding, optimal reimbursement, and regulatory compliance.
Frequently Asked Questions
Common questions about ICD-10 coding for Alpha-1 Antitrypsin Deficiency, with expert answers to help guide accurate code selection and documentation.
Documentation Templates for Alpha-1 Antitrypsin Deficiency
Use these documentation templates to ensure complete and accurate documentation for Alpha-1 Antitrypsin Deficiency. These templates include all required elements for proper coding and billing.
Pulmonary presentation of AATD
Specialty: PulmonologyRequired Elements
- Family history
- Specific symptoms
- Lab results
- Imaging findings
Example Documentation
Examples: Poor vs. Good Documentation
Poor Documentation Example
Good Documentation Example
Explanation
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