Back to HomeBeta

ICD-10 Coding for Antiphospholipid Antibody Syndrome(D68.61)

Complete ICD-10-CM coding and documentation guide for Antiphospholipid Antibody Syndrome. Includes clinical validation requirements, documentation requirements, and coding pitfalls.

Also known as:

APSHughes Syndrome

Related ICD-10 Code Ranges

Complete code families applicable to Antiphospholipid Antibody Syndrome

D68.6-D68.69Primary Range

Other thrombophilia

This range includes codes for various types of thrombophilia, including antiphospholipid syndrome.

Key Information: ICD-10 code for antiphospholipid antibody syndrome

Essential facts and insights about Antiphospholipid Antibody Syndrome

The ICD-10 code for antiphospholipid antibody syndrome is D68.61, used when APS is confirmed by clinical and laboratory criteria.

Primary ICD-10-CM Code for antiphospholipid antibody syndrome

Antiphospholipid syndrome
Billable Code

Decision Criteria

clinical Criteria

  • Presence of thrombosis or pregnancy morbidity with confirmed antibodies

documentation Criteria

  • Documented lab results showing persistent antibodies

Applicable To

  • Primary antiphospholipid syndrome
  • Secondary antiphospholipid syndrome

Excludes

  • Lupus anticoagulant syndrome (D68.62)

Clinical Validation Requirements

  • Persistent presence of lupus anticoagulant, anticardiolipin, or anti-β2GPI antibodies on two occasions 12 weeks apart
  • Clinical criteria such as thrombosis or pregnancy morbidity

Code-Specific Risks

  • Incorrectly coding transient antibody presence as APS
  • Failure to document persistence of antibodies

Coding Notes

  • Ensure documentation supports the persistence of antibodies and clinical manifestations.

Ancillary Codes

Additional codes that should be used in conjunction with the main diagnosis codes when applicable.

Other specified diseases and conditions complicating pregnancy, childbirth and the puerperium

O99.89
Use when APS complicates pregnancy.

Differential Codes

Alternative codes to consider when ruling out similar conditions to the primary diagnosis.

Lupus anticoagulant syndrome

D68.62
Use when lupus anticoagulant is present without other APS criteria.

Documentation & Coding Risks

Avoid these common documentation and coding issues when documenting Antiphospholipid Antibody Syndrome to ensure proper reimbursement, maintain compliance, and reduce audit risk. These guidelines are particularly important when using ICD-10 code D68.61.

Impact

Clinical: May lead to misdiagnosis and inappropriate treatment., Regulatory: Non-compliance with coding standards., Financial: Potential claim denials or audits.

Mitigation Strategy

Ensure lab tests are repeated and documented., Educate staff on APS diagnostic criteria.

Impact

Reimbursement: Incorrect coding may lead to denied claims., Compliance: Non-compliance with coding guidelines., Data Quality: Inaccurate clinical data representation.

Mitigation Strategy

Ensure documentation includes two positive tests 12 weeks apart.

Impact

High risk of audit if APS is coded without documented lab confirmation.

Mitigation Strategy

Ensure all APS diagnoses are supported by lab results showing persistent antibodies.

Documentation errors, coding pitfalls, and audit risks are interconnected aspects of medical coding and billing. Addressing all three areas helps ensure accurate coding, optimal reimbursement, and regulatory compliance.

Frequently Asked Questions

Common questions about ICD-10 coding for Antiphospholipid Antibody Syndrome, with expert answers to help guide accurate code selection and documentation.

Documentation Templates for Antiphospholipid Antibody Syndrome

Use these documentation templates to ensure complete and accurate documentation for Antiphospholipid Antibody Syndrome. These templates include all required elements for proper coding and billing.

APS with recurrent thrombosis

Specialty: Rheumatology

Required Elements

  • Diagnosis confirmation with lab results
  • Clinical manifestations
  • Treatment plan

Example Documentation

Assessment: Primary antiphospholipid syndrome confirmed by lupus anticoagulant positive via dRVVT on [date] and [date]. Current manifestations include recurrent DVT.

Examples: Poor vs. Good Documentation

Poor Documentation Example
Patient has clotting disorder, will start anticoagulation.
Good Documentation Example
Primary antiphospholipid syndrome confirmed by lupus anticoagulant positive via dRVVT (ratio 1.8) on 1/1/25 and 4/1/25. Recurrent DVT despite aspirin therapy.
Explanation
The good example provides specific lab results and clinical manifestations, supporting the diagnosis.

Need help with ICD-10 coding for Antiphospholipid Antibody Syndrome? Ask your questions below.

Ask about any ICD-10 CM code, or paste a medical note

We build tools for
clinician happiness.

Learn More at Freed.ai
Back to HomeBeta

Built by Freed

Try Freed for free for 7 days.

Learn more