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ICD-10 Coding for Autoimmune Encephalitis(G04.81)

Complete ICD-10-CM coding and documentation guide for Autoimmune Encephalitis. Includes clinical validation requirements, documentation requirements, and coding pitfalls.

Also known as:

AIEImmune-mediated Encephalitis

Related ICD-10 Code Ranges

Complete code families applicable to Autoimmune Encephalitis

G04.80-G04.89Primary Range

Other Encephalitis and Encephalomyelitis

This range includes specific codes for various types of encephalitis, including autoimmune encephalitis.

Key Information: ICD-10 code for autoimmune encephalitis

Essential facts and insights about Autoimmune Encephalitis

The ICD-10 code for autoimmune encephalitis is G04.81, used for other encephalitis and encephalomyelitis.

Primary ICD-10-CM Code for autoimmune encephalitis

Other encephalitis and encephalomyelitis
Billable Code

Decision Criteria

clinical Criteria

  • Presence of specific autoantibodies in CSF or serum.

documentation Criteria

  • Document subacute onset and exclusion of infectious causes.

Applicable To

  • Autoimmune encephalitis

Excludes

  • Infectious encephalitis (A81.9)

Clinical Validation Requirements

  • Subacute onset of symptoms
  • CSF autoantibodies
  • MRI findings of limbic system hyperintensity

Code-Specific Risks

  • Incorrect use can lead to insurance denials if documentation does not support autoimmune etiology.

Coding Notes

  • Ensure documentation specifies autoimmune nature to avoid unspecified codes.

Ancillary Codes

Additional codes that should be used in conjunction with the main diagnosis codes when applicable.

Abnormal CSF findings

R94.8
Use with CSF pleocytosis or elevated IgG index.

Personal history of autoimmune disease

Z86.59
Use if AIE is secondary to a systemic autoimmune disorder.

Differential Codes

Alternative codes to consider when ruling out similar conditions to the primary diagnosis.

Unspecified encephalitis

G04.90
Use only if autoimmune etiology is unconfirmed.

Delirium

F05
Use for non-inflammatory encephalopathy.

Documentation & Coding Risks

Avoid these common documentation and coding issues when documenting Autoimmune Encephalitis to ensure proper reimbursement, maintain compliance, and reduce audit risk. These guidelines are particularly important when using ICD-10 code G04.81.

Impact

Clinical: Misdiagnosis risk., Regulatory: Non-compliance with coding standards., Financial: Potential for claim denials.

Mitigation Strategy

Ensure thorough differential diagnosis is documented.

Impact

Reimbursement: Potential for reduced reimbursement due to unspecified coding., Compliance: Non-compliance with coding guidelines., Data Quality: Decreased accuracy in health data reporting.

Mitigation Strategy

Use G04.81 with appropriate documentation of autoimmune features.

Impact

Lack of specific documentation can lead to audit issues.

Mitigation Strategy

Ensure all clinical findings and test results are documented.

Documentation errors, coding pitfalls, and audit risks are interconnected aspects of medical coding and billing. Addressing all three areas helps ensure accurate coding, optimal reimbursement, and regulatory compliance.

Frequently Asked Questions

Common questions about ICD-10 coding for Autoimmune Encephalitis, with expert answers to help guide accurate code selection and documentation.

Documentation Templates for Autoimmune Encephalitis

Use these documentation templates to ensure complete and accurate documentation for Autoimmune Encephalitis. These templates include all required elements for proper coding and billing.

Neurology H&P for suspected autoimmune encephalitis

Specialty: Neurology

Required Elements

  • Chief complaint
  • History of present illness
  • Neurological examination
  • Diagnostic test results

Example Documentation

Patient presents with subacute memory loss and seizures. CSF shows anti-NMDA-R antibodies. MRI reveals limbic hyperintensity.

Examples: Poor vs. Good Documentation

Poor Documentation Example
Encephalitis, treat with steroids.
Good Documentation Example
Subacute encephalitis with anti-LGI1 antibodies confirmed by CSF analysis, responsive to immunotherapy.
Explanation
The good example provides specific clinical details and confirms autoimmune etiology.

Need help with ICD-10 coding for Autoimmune Encephalitis? Ask your questions below.

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