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ICD-10 Coding for Autonomic Dysfunction(G90.0, G90.A, E11.43)

Complete ICD-10-CM coding and documentation guide for Autonomic Dysfunction. Includes clinical validation requirements, documentation requirements, and coding pitfalls.

Also known as:

DysautonomiaAutonomic Neuropathy

Related ICD-10 Code Ranges

Complete code families applicable to Autonomic Dysfunction

G90Primary Range

Disorders of autonomic nervous system

This range includes various autonomic disorders such as idiopathic neuropathy and POTS.

Type 2 diabetes mellitus with diabetic autonomic (poly)neuropathy

Used when autonomic dysfunction is due to diabetes.

Code Comparison: When to Use Each Code

Compare key differences between these codes to ensure accurate selection

CodeDescriptionWhen to UseKey Documentation
G90.0Idiopathic peripheral autonomic neuropathyUse when autonomic neuropathy is idiopathic and not linked to other conditions.
  • QSART shows reduced distal sweat volume
  • No diabetes or amyloidosis
G90.APostural orthostatic tachycardia syndrome (POTS)Use when all POTS criteria are met and documented.
  • Sustained HR increase ≥30 bpm within 10 mins standing
  • Absence of orthostatic hypotension
E11.43Type 2 diabetes mellitus with diabetic autonomic (poly)neuropathyUse when autonomic dysfunction is due to diabetes.
  • Confirmed diabetes diagnosis
  • Autonomic symptoms linked to diabetes

Clinical Decision Support

Always review the patient's clinical documentation thoroughly. When in doubt, choose the more specific code and ensure documentation supports it.

Key Information: ICD-10 code for POTS

Essential facts and insights about Autonomic Dysfunction

The ICD-10 code for Postural Orthostatic Tachycardia Syndrome (POTS) is G90.A.

Primary ICD-10-CM Codes for autonomic dysfunction

Idiopathic peripheral autonomic neuropathy
Non-billable Code

Decision Criteria

clinical Criteria

  • Confirmed idiopathic nature through testing

Applicable To

  • Idiopathic autonomic neuropathy

Excludes

  • Diabetic autonomic neuropathy (E11.43)

Clinical Validation Requirements

  • QSART shows reduced distal sweat volume
  • No diabetes or amyloidosis

Code-Specific Risks

  • Misclassification if underlying cause is not ruled out

Coding Notes

  • Ensure idiopathic nature is documented.

Differential Codes

Alternative codes to consider when ruling out similar conditions to the primary diagnosis.

Type 2 diabetes mellitus with diabetic autonomic (poly)neuropathy

E11.43
Use E11.43 if diabetes is the underlying cause.

Orthostatic hypotension

I95.1
Use I95.1 if hypotension is present.

Documentation & Coding Risks

Avoid these common documentation and coding issues when documenting Autonomic Dysfunction to ensure proper reimbursement, maintain compliance, and reduce audit risk. These guidelines are particularly important when using ICD-10 code G90.0.

Impact

Clinical: Misdiagnosis risk, Regulatory: Non-compliance with documentation standards, Financial: Potential claim denials

Mitigation Strategy

Use specific symptom descriptions, Include test results

Impact

Reimbursement: Incorrect coding may lead to reduced reimbursement., Compliance: Non-compliance with coding guidelines., Data Quality: Inaccurate data representation.

Mitigation Strategy

Use G90.A for POTS when criteria are met.

Impact

Incomplete documentation of POTS criteria.

Mitigation Strategy

Use templates to ensure all criteria are documented.

Documentation errors, coding pitfalls, and audit risks are interconnected aspects of medical coding and billing. Addressing all three areas helps ensure accurate coding, optimal reimbursement, and regulatory compliance.

Frequently Asked Questions

Common questions about ICD-10 coding for Autonomic Dysfunction, with expert answers to help guide accurate code selection and documentation.

Documentation Templates for Autonomic Dysfunction

Use these documentation templates to ensure complete and accurate documentation for Autonomic Dysfunction. These templates include all required elements for proper coding and billing.

POTS Diagnosis

Specialty: Cardiology

Required Elements

  • Orthostatic symptoms
  • HR/BP measurements
  • Exclusion of other causes

Example Documentation

Patient presents with lightheadedness upon standing. HR increased from 68 supine to 112 standing at 3 mins, sustained for 10 mins. No dehydration or anemia.

Examples: Poor vs. Good Documentation

Poor Documentation Example
Patient has POTS.
Good Documentation Example
HR increased from 68 supine to 112 standing at 3 mins, sustained for 10 mins. Ferritin 45 ng/mL, TSH 2.1. No dehydration.
Explanation
The good example provides specific HR changes and excludes other causes.

Need help with ICD-10 coding for Autonomic Dysfunction? Ask your questions below.

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