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ICD-10 Coding for Autosomal Dominant Polycystic Kidney Disease(Q61.2, Q61.3)

Complete ICD-10-CM coding and documentation guide for Autosomal Dominant Polycystic Kidney Disease. Includes clinical validation requirements, documentation requirements, and coding pitfalls.

Also known as:

ADPKDPolycystic Kidney Disease Type 1Polycystic Kidney Disease Type 2

Related ICD-10 Code Ranges

Complete code families applicable to Autosomal Dominant Polycystic Kidney Disease

Q61.2-Q61.3Primary Range

Polycystic kidney disease codes

These codes cover the spectrum of polycystic kidney diseases, with Q61.2 specifically for ADPKD.

Code Comparison: When to Use Each Code

Compare key differences between these codes to ensure accurate selection

CodeDescriptionWhen to UseKey Documentation
Q61.2Autosomal dominant polycystic kidney diseaseUse when ADPKD is confirmed through genetic testing or meets clinical criteria.
  • Genetic testing showing PKD1 or PKD2 mutations
  • Imaging showing multiple bilateral renal cysts
  • Family history of ADPKD
Q61.3Polycystic kidney, unspecifiedUse when documentation lacks confirmation of inheritance pattern.
  • Imaging showing renal cysts without family history or genetic confirmation

Clinical Decision Support

Always review the patient's clinical documentation thoroughly. When in doubt, choose the more specific code and ensure documentation supports it.

Key Information: ICD-10 code for autosomal dominant polycystic kidney disease

Essential facts and insights about Autosomal Dominant Polycystic Kidney Disease

The ICD-10 code for autosomal dominant polycystic kidney disease is Q61.2, used when confirmed by genetic testing or clinical criteria.

Primary ICD-10-CM Codes for autosomal dominant polycystic kidney disease

Autosomal dominant polycystic kidney disease
Billable Code

Decision Criteria

clinical Criteria

  • Presence of ≥3 bilateral renal cysts and family history

coding Criteria

  • Confirmed genetic testing for PKD1 or PKD2

Applicable To

  • Confirmed ADPKD with genetic testing
  • ≥3 bilateral renal cysts with family history

Excludes

  • Autosomal recessive polycystic kidney disease (Q61.19)

Clinical Validation Requirements

  • Genetic testing showing PKD1 or PKD2 mutations
  • Imaging showing multiple bilateral renal cysts
  • Family history of ADPKD

Code-Specific Risks

  • Misclassification with ARPKD
  • Undercoding due to lack of genetic confirmation

Coding Notes

  • Ensure documentation supports the use of Q61.2 with genetic or imaging evidence.

Ancillary Codes

Additional codes that should be used in conjunction with the main diagnosis codes when applicable.

Other specified disorders of kidney

N28.89
Use for complications such as cyst infection or hemorrhage.

Differential Codes

Alternative codes to consider when ruling out similar conditions to the primary diagnosis.

Autosomal recessive polycystic kidney disease

Q61.19
ARPKD typically presents in infancy with different genetic markers.

Autosomal dominant polycystic kidney disease

Q61.2
Use Q61.2 when ADPKD is confirmed.

Documentation & Coding Risks

Avoid these common documentation and coding issues when documenting Autosomal Dominant Polycystic Kidney Disease to ensure proper reimbursement, maintain compliance, and reduce audit risk. These guidelines are particularly important when using ICD-10 code Q61.2.

Impact

Clinical: May lead to misdiagnosis or inappropriate treatment., Regulatory: Non-compliance with coding standards., Financial: Potential for denied claims or reduced reimbursement.

Mitigation Strategy

Always document family history for suspected genetic conditions., Use templates to ensure comprehensive documentation.

Impact

Reimbursement: Incorrect coding can lead to denied claims., Compliance: Misclassification affects compliance with coding standards., Data Quality: Impacts accuracy of patient records and data analytics.

Mitigation Strategy

Verify inheritance pattern and age of onset to differentiate.

Impact

Reimbursement: May affect DRG assignment and reimbursement rates., Compliance: Leads to potential audit issues., Data Quality: Reduces specificity and accuracy of health data.

Mitigation Strategy

Ensure documentation supports specific coding with genetic or imaging evidence.

Impact

Lack of documentation for genetic testing results can lead to audit issues.

Mitigation Strategy

Ensure all genetic testing results are included in patient records.

Documentation errors, coding pitfalls, and audit risks are interconnected aspects of medical coding and billing. Addressing all three areas helps ensure accurate coding, optimal reimbursement, and regulatory compliance.

Frequently Asked Questions

Common questions about ICD-10 coding for Autosomal Dominant Polycystic Kidney Disease, with expert answers to help guide accurate code selection and documentation.

Documentation Templates for Autosomal Dominant Polycystic Kidney Disease

Use these documentation templates to ensure complete and accurate documentation for Autosomal Dominant Polycystic Kidney Disease. These templates include all required elements for proper coding and billing.

Initial ADPKD Diagnosis

Specialty: Nephrology

Required Elements

  • Family history
  • Imaging results
  • Genetic testing
  • Blood pressure readings

Example Documentation

Patient presents with multiple bilateral renal cysts, family history of ADPKD, and pending genetic testing.

Examples: Poor vs. Good Documentation

Poor Documentation Example
Patient has kidney cysts.
Good Documentation Example
Ultrasound reveals ≥3 bilateral renal cysts, hepatic cysts, and family history of ESRD in father with ADPKD.
Explanation
The good example provides specific imaging and family history details necessary for accurate coding.

Need help with ICD-10 coding for Autosomal Dominant Polycystic Kidney Disease? Ask your questions below.

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