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ICD-10 Coding for Cardiomyopathy(I42.0, I42.1)

Complete ICD-10-CM coding and documentation guide for Cardiomyopathy. Includes clinical validation requirements, documentation requirements, and coding pitfalls.

Also known as:

Heart Muscle DiseaseMyocardial Disease

Related ICD-10 Code Ranges

Complete code families applicable to Cardiomyopathy

I42-I43Primary Range

Cardiomyopathy

This range includes all types of cardiomyopathy, which are primary conditions affecting the heart muscle.

Ischemic Cardiomyopathy

Ischemic cardiomyopathy is related but distinct, requiring separate coding.

Code Comparison: When to Use Each Code

Compare key differences between these codes to ensure accurate selection

CodeDescriptionWhen to UseKey Documentation
I42.0Dilated CardiomyopathyUse when echocardiogram confirms dilated cardiomyopathy with reduced ejection fraction.
  • LVEF <40%
  • Ventricular dilation on echocardiogram
I42.1Obstructive Hypertrophic CardiomyopathyUse when echocardiogram shows obstructive hypertrophic changes with significant gradient.
  • Subaortic gradient ≥30 mmHg
  • Genetic testing for MYH7/MYBPC3 mutation

Clinical Decision Support

Always review the patient's clinical documentation thoroughly. When in doubt, choose the more specific code and ensure documentation supports it.

Key Information: ICD-10 code for dilated cardiomyopathy

Essential facts and insights about Cardiomyopathy

The ICD-10 code for dilated cardiomyopathy is I42.0, used when echocardiogram confirms ventricular dilation and reduced ejection fraction.

Primary ICD-10-CM Codes for cardiomyopathy

Dilated Cardiomyopathy
Billable Code

Decision Criteria

clinical Criteria

  • Echocardiogram showing ventricular dilation and reduced ejection fraction.

Applicable To

  • Congestive cardiomyopathy

Excludes

  • Ischemic cardiomyopathy (I25.5)

Clinical Validation Requirements

  • LVEF <40%
  • Ventricular dilation on echocardiogram

Code-Specific Risks

  • Incorrectly coding as unspecified cardiomyopathy (I42.9)

Coding Notes

  • Ensure documentation specifies 'dilated' to avoid unspecified coding.

Ancillary Codes

Additional codes that should be used in conjunction with the main diagnosis codes when applicable.

Heart Failure

I50.-
Use to specify heart failure type if present with cardiomyopathy.

Hypertensive Heart Disease

I11.-
Use if hypertensive heart disease is present.

Differential Codes

Alternative codes to consider when ruling out similar conditions to the primary diagnosis.

Ischemic Cardiomyopathy

I25.5
Presence of coronary artery disease and myocardial infarction history.

Non-obstructive Hypertrophic Cardiomyopathy

I42.2
Absence of significant subaortic gradient.

Documentation & Coding Risks

Avoid these common documentation and coding issues when documenting Cardiomyopathy to ensure proper reimbursement, maintain compliance, and reduce audit risk. These guidelines are particularly important when using ICD-10 code I42.0.

Impact

Clinical: Impacts treatment decisions and monitoring., Regulatory: May lead to audit issues., Financial: Affects reimbursement for heart failure management.

Mitigation Strategy

Always include ejection fraction in documentation., Use templates to ensure completeness.

Impact

Reimbursement: May lead to reduced reimbursement rates., Compliance: Increases risk of audit due to lack of specificity., Data Quality: Decreases accuracy of clinical data.

Mitigation Strategy

Ensure documentation specifies the type of cardiomyopathy.

Impact

Use of unspecified cardiomyopathy codes increases audit risk.

Mitigation Strategy

Document specific type and associated clinical findings.

Documentation errors, coding pitfalls, and audit risks are interconnected aspects of medical coding and billing. Addressing all three areas helps ensure accurate coding, optimal reimbursement, and regulatory compliance.

Frequently Asked Questions

Common questions about ICD-10 coding for Cardiomyopathy, with expert answers to help guide accurate code selection and documentation.

Documentation Templates for Cardiomyopathy

Use these documentation templates to ensure complete and accurate documentation for Cardiomyopathy. These templates include all required elements for proper coding and billing.

Cardiology Progress Note

Specialty: Cardiology

Required Elements

  • Assessment of cardiomyopathy type
  • Echocardiogram findings
  • Ejection fraction percentage
  • Treatment plan

Example Documentation

Patient presents with dilated cardiomyopathy, LVEF 35% on echocardiogram. Plan includes ACE inhibitors and beta-blockers.

Examples: Poor vs. Good Documentation

Poor Documentation Example
Cardiomyopathy noted.
Good Documentation Example
Dilated cardiomyopathy with LVEF 35% on echocardiogram.
Explanation
The good example provides specific type and quantitative data, improving coding accuracy.

Need help with ICD-10 coding for Cardiomyopathy? Ask your questions below.

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