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ICD-10 Coding for Cobalamin Deficiency(D51.0, D51.1, D51.8, D51.9)

Complete ICD-10-CM coding and documentation guide for Cobalamin Deficiency. Includes clinical validation requirements, documentation requirements, and coding pitfalls.

Also known as:

Vitamin B12 DeficiencyPernicious Anemia

Related ICD-10 Code Ranges

Complete code families applicable to Cobalamin Deficiency

D51.0-D51.9Primary Range

Vitamin B12 deficiency anemia

This range includes all codes related to vitamin B12 deficiency anemia, including pernicious anemia and other specified and unspecified B12 deficiencies.

Code Comparison: When to Use Each Code

Compare key differences between these codes to ensure accurate selection

CodeDescriptionWhen to UseKey Documentation
D51.0Vitamin B12 deficiency anemia due to intrinsic factor deficiencyUse when pernicious anemia is confirmed with intrinsic factor deficiency.
  • Autoimmune destruction of gastric parietal cells
  • Positive intrinsic factor antibody
  • Serum B12 <200 pg/mL
  • + 1 more
D51.1Vitamin B12 deficiency anemia due to selective vitamin B12 malabsorption with proteinuriaUse for pediatric cases with selective B12 malabsorption and renal involvement.
  • Proteinuria >300 mg/day
  • Genetic confirmation of cubilin/amnioless defects
  • Serum B12 <150 pg/mL
D51.8Other vitamin B12 deficiency anemiaUse for B12 deficiencies due to non-autoimmune malabsorption.
  • Documented malabsorption risk (e.g., gastrectomy, chronic PPI use)
  • Serum B12 <200 pg/mL
D51.9Vitamin B12 deficiency anemia, unspecifiedUse when the specific cause of B12 deficiency is not determined.
  • Low serum B12 without confirmed etiology

Clinical Decision Support

Always review the patient's clinical documentation thoroughly. When in doubt, choose the more specific code and ensure documentation supports it.

Key Information: ICD-10 code for cobalamin deficiency

Essential facts and insights about Cobalamin Deficiency

The ICD-10 code for cobalamin deficiency is primarily D51.0, used for vitamin B12 deficiency anemia due to intrinsic factor deficiency.

Primary ICD-10-CM Codes for cobalamin deficiency

Vitamin B12 deficiency anemia due to intrinsic factor deficiency
Billable Code

Decision Criteria

clinical Criteria

  • Presence of positive intrinsic factor antibody

documentation Criteria

  • Documented autoimmune gastritis

Applicable To

  • Pernicious anemia

Excludes

  • Other specified vitamin B12 deficiency anemia (D51.8)

Clinical Validation Requirements

  • Autoimmune destruction of gastric parietal cells
  • Positive intrinsic factor antibody
  • Serum B12 <200 pg/mL
  • MMA >0.4 µmol/L

Code-Specific Risks

  • Incorrectly using D51.9 when specific etiology is known.

Coding Notes

  • Ensure documentation of intrinsic factor deficiency is present.

Ancillary Codes

Additional codes that should be used in conjunction with the main diagnosis codes when applicable.

Other specified abnormal findings of blood chemistry

R79.8
Use to indicate elevated MMA levels.

Differential Codes

Alternative codes to consider when ruling out similar conditions to the primary diagnosis.

Other vitamin B12 deficiency anemia

D51.8
Use D51.8 for B12 deficiencies due to malabsorption not related to intrinsic factor deficiency.

Vitamin B12 deficiency anemia due to intrinsic factor deficiency

D51.0
Use D51.0 when intrinsic factor deficiency is confirmed.

Documentation & Coding Risks

Avoid these common documentation and coding issues when documenting Cobalamin Deficiency to ensure proper reimbursement, maintain compliance, and reduce audit risk. These guidelines are particularly important when using ICD-10 code D51.0.

Impact

Clinical: Leads to inappropriate treatment plans., Regulatory: Non-compliance with coding standards., Financial: Potential for denied claims.

Mitigation Strategy

Ensure thorough documentation of lab results and clinical findings., Use templates to guide documentation.

Impact

Reimbursement: May result in denied claims or lower reimbursement., Compliance: Non-compliance with coding guidelines., Data Quality: Decreases accuracy of medical records.

Mitigation Strategy

Ensure documentation specifies the cause of B12 deficiency.

Impact

High risk of audit if D51.9 is used without proper justification.

Mitigation Strategy

Ensure specific etiology is documented and coded appropriately.

Documentation errors, coding pitfalls, and audit risks are interconnected aspects of medical coding and billing. Addressing all three areas helps ensure accurate coding, optimal reimbursement, and regulatory compliance.

Frequently Asked Questions

Common questions about ICD-10 coding for Cobalamin Deficiency, with expert answers to help guide accurate code selection and documentation.

Documentation Templates for Cobalamin Deficiency

Use these documentation templates to ensure complete and accurate documentation for Cobalamin Deficiency. These templates include all required elements for proper coding and billing.

Endocrinology Clinic Assessment

Specialty: Endocrinology

Required Elements

  • Serum B12 levels
  • MMA and homocysteine levels
  • Intrinsic factor antibody status
  • Gastric pathology findings

Example Documentation

Assessment: Serum B12: ___ pg/mL, MMA: ___ µmol/L, IF Antibody: ☐ Positive ☐ Negative.

Examples: Poor vs. Good Documentation

Poor Documentation Example
Patient has B12 deficiency. Start injections.
Good Documentation Example
Macrocytic anemia with serum B12 110 pg/mL and MMA 0.68 µmol/L. Etiology: Atrophic gastritis confirmed by endoscopy.
Explanation
The good example provides specific lab values and etiology, supporting accurate coding.

Need help with ICD-10 coding for Cobalamin Deficiency? Ask your questions below.

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