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ICD-10 Coding for Cystic Fibrosis(E84.0, E84.19)

Complete ICD-10-CM coding and documentation guide for Cystic Fibrosis. Includes clinical validation requirements, documentation requirements, and coding pitfalls.

Also known as:

CFMucoviscidosis

Related ICD-10 Code Ranges

Complete code families applicable to Cystic Fibrosis

E84Primary Range

Cystic fibrosis

This range includes all codes related to cystic fibrosis and its manifestations.

Code Comparison: When to Use Each Code

Compare key differences between these codes to ensure accurate selection

CodeDescriptionWhen to UseKey Documentation
E84.0Cystic fibrosis with pulmonary manifestationsUse when cystic fibrosis presents with pulmonary symptoms such as chronic cough and bronchiectasis.
  • Chronic cough
  • Sputum production
  • Bronchiectasis on CT
  • + 1 more
E84.19Cystic fibrosis with other intestinal manifestationsUse when cystic fibrosis presents with intestinal symptoms such as steatorrhea or meconium ileus.
  • Steatorrhea
  • Fecal elastase <200 µg/g
  • Recurrent pancreatitis

Clinical Decision Support

Always review the patient's clinical documentation thoroughly. When in doubt, choose the more specific code and ensure documentation supports it.

Key Information: ICD-10 code for cystic fibrosis

Essential facts and insights about Cystic Fibrosis

The ICD-10 code for cystic fibrosis with pulmonary manifestations is E84.0, while E84.19 is used for intestinal manifestations.

Primary ICD-10-CM Codes for cystic fibrosis

Cystic fibrosis with pulmonary manifestations
Billable Code

Decision Criteria

clinical Criteria

  • Presence of chronic cough and sputum production with confirmed CF diagnosis.

Applicable To

  • Chronic lung disease due to cystic fibrosis

Excludes

  • Cystic fibrosis with intestinal manifestations (E84.19)

Clinical Validation Requirements

  • Chronic cough
  • Sputum production
  • Bronchiectasis on CT
  • FEV1 <70% predicted

Code-Specific Risks

  • Ensure documentation specifies pulmonary involvement to avoid incorrect coding.

Coding Notes

  • Ensure to document specific pulmonary manifestations and any identified organisms.

Ancillary Codes

Additional codes that should be used in conjunction with the main diagnosis codes when applicable.

Pseudomonas (aeruginosa) as the cause of diseases classified elsewhere

B96.5
Use when Pseudomonas is identified in cultures.

Differential Codes

Alternative codes to consider when ruling out similar conditions to the primary diagnosis.

Other interstitial pulmonary diseases with fibrosis

J84.1
Use if fibrosis is not due to cystic fibrosis.

Fecal impaction

K56.41
Use if obstruction is not due to cystic fibrosis.

Documentation & Coding Risks

Avoid these common documentation and coding issues when documenting Cystic Fibrosis to ensure proper reimbursement, maintain compliance, and reduce audit risk. These guidelines are particularly important when using ICD-10 code E84.0.

Impact

Clinical: Inaccurate representation of patient's condition., Regulatory: Potential non-compliance with ICD-10 coding guidelines., Financial: May result in reduced reimbursement.

Mitigation Strategy

Educate providers on the importance of detailed documentation., Implement regular chart audits to ensure compliance.

Impact

Reimbursement: May lead to lower reimbursement due to lack of specificity., Compliance: Non-compliance with coding guidelines., Data Quality: Reduces accuracy of clinical data.

Mitigation Strategy

Query provider to specify pulmonary or intestinal involvement.

Impact

Use of unspecified codes like E84.9 can trigger audits.

Mitigation Strategy

Ensure documentation specifies all manifestations and complications.

Documentation errors, coding pitfalls, and audit risks are interconnected aspects of medical coding and billing. Addressing all three areas helps ensure accurate coding, optimal reimbursement, and regulatory compliance.

Frequently Asked Questions

Common questions about ICD-10 coding for Cystic Fibrosis, with expert answers to help guide accurate code selection and documentation.

Documentation Templates for Cystic Fibrosis

Use these documentation templates to ensure complete and accurate documentation for Cystic Fibrosis. These templates include all required elements for proper coding and billing.

Pulmonary exacerbation in cystic fibrosis

Specialty: Pulmonology

Required Elements

  • Increased cough
  • Sputum production
  • FEV1 decline
  • Sputum culture results

Example Documentation

Patient presents with increased cough and sputum production. FEV1 declined from 65% to 52%. Sputum culture positive for Pseudomonas aeruginosa.

Examples: Poor vs. Good Documentation

Poor Documentation Example
CF with lung issues.
Good Documentation Example
Cystic fibrosis with pulmonary exacerbation characterized by increased sputum production and Pseudomonas aeruginosa identified via sputum culture.
Explanation
The good example provides specific details about the pulmonary manifestations and identifies the organism, supporting accurate coding.

Need help with ICD-10 coding for Cystic Fibrosis? Ask your questions below.

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