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ICD-10 Coding for Factor V Leiden Deficiency(D68.51, D68.59)

Complete ICD-10-CM coding and documentation guide for Factor V Leiden Deficiency. Includes clinical validation requirements, documentation requirements, and coding pitfalls.

Also known as:

Activated Protein C ResistanceFactor V Leiden Mutationfactor v mutation

Related ICD-10 Code Ranges

Complete code families applicable to Factor V Leiden Deficiency

D68.5-D68.69Primary Range

Other Coagulation Defects

This range includes codes for various coagulation disorders, including Factor V Leiden.

Code Comparison: When to Use Each Code

Compare key differences between these codes to ensure accurate selection

CodeDescriptionWhen to UseKey Documentation
D68.51Activated protein C resistanceUse when Factor V Leiden mutation is confirmed by lab tests.
  • Positive DNA test (PCR) for Factor V Leiden
  • APC resistance assay showing resistance
D68.59Other primary thrombophiliaUse when hereditary thrombophilia is suspected but not confirmed as Factor V Leiden.
  • Family history of thrombophilia
  • Absence of specific APC resistance confirmation

Clinical Decision Support

Always review the patient's clinical documentation thoroughly. When in doubt, choose the more specific code and ensure documentation supports it.

Key Information: ICD-10 code for Factor V Leiden deficiency

Essential facts and insights about Factor V Leiden Deficiency

The ICD-10 code for Factor V Leiden deficiency is D68.51, used for confirmed activated protein C resistance.

Primary ICD-10-CM Codes for factor vomiting leiden deficiency

Activated protein C resistance
Billable Code

Decision Criteria

clinical Criteria

  • Confirmed Factor V Leiden mutation via PCR

documentation Criteria

  • APC resistance assay results

Applicable To

  • Factor V Leiden mutation

Excludes

  • Antiphospholipid syndrome (D68.62)

Clinical Validation Requirements

  • Positive DNA test (PCR) for Factor V Leiden
  • APC resistance assay showing resistance

Code-Specific Risks

  • Misclassification if not confirmed by lab tests

Coding Notes

  • Ensure documentation specifies the type of mutation and method of confirmation.

Ancillary Codes

Additional codes that should be used in conjunction with the main diagnosis codes when applicable.

Family history of thrombophilia

Z84.81
Use to indicate family history of thrombophilia.

Differential Codes

Alternative codes to consider when ruling out similar conditions to the primary diagnosis.

Other primary thrombophilia

D68.59
Use D68.59 for hereditary thrombophilia without specific APC resistance confirmation.

Activated protein C resistance

D68.51
Use D68.51 when Factor V Leiden mutation is confirmed.

Documentation & Coding Risks

Avoid these common documentation and coding issues when documenting Factor V Leiden Deficiency to ensure proper reimbursement, maintain compliance, and reduce audit risk. These guidelines are particularly important when using ICD-10 code D68.51.

Impact

Clinical: May lead to inappropriate treatment plans., Regulatory: Non-compliance with coding standards., Financial: Potential claim denials or audits.

Mitigation Strategy

Ensure detailed documentation of genetic testing results, Specify type of thrombophilia

Impact

Reimbursement: Incorrect coding may lead to denied claims., Compliance: Non-compliance with coding standards., Data Quality: Inaccurate patient records and data reporting.

Mitigation Strategy

Ensure lab confirmation of Factor V Leiden before using D68.51.

Impact

Using incorrect codes for confirmed genetic mutations.

Mitigation Strategy

Regular training on genetic testing documentation and coding.

Documentation errors, coding pitfalls, and audit risks are interconnected aspects of medical coding and billing. Addressing all three areas helps ensure accurate coding, optimal reimbursement, and regulatory compliance.

Frequently Asked Questions

Common questions about ICD-10 coding for Factor V Leiden Deficiency, with expert answers to help guide accurate code selection and documentation.

Documentation Templates for Factor V Leiden Deficiency

Use these documentation templates to ensure complete and accurate documentation for Factor V Leiden Deficiency. These templates include all required elements for proper coding and billing.

Hematology Consult for Factor V Leiden

Specialty: Hematology

Required Elements

  • Chief Complaint
  • History of Present Illness
  • Family History
  • Lab Results
  • Assessment and Plan

Example Documentation

45F with heterozygous Factor V Leiden (G1691A variant per Quest Diagnostics PCR, 03/2025) presents for anticoagulation management post-LE DVT. No personal/family history of arterial clots. APC resistance ratio: 1.8 (ref >2.0). Plan: Continue rivaroxaban 20mg daily.

Examples: Poor vs. Good Documentation

Poor Documentation Example
Clotting disorder – monitor
Good Documentation Example
Heterozygous Factor V Leiden (PCR-confirmed) with APC resistance ratio 1.7; on lifelong anticoagulation due to recurrent provoked DVTs
Explanation
The good example provides specific genetic confirmation and treatment plan, improving clarity and compliance.

Need help with ICD-10 coding for Factor V Leiden Deficiency? Ask your questions below.

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