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ICD-10 Coding for Fibromuscular Dysplasia(I77.3)

Complete ICD-10-CM coding and documentation guide for Fibromuscular Dysplasia. Includes clinical validation requirements, documentation requirements, and coding pitfalls.

Also known as:

FMDArterial Fibromuscular Dysplasia

Related ICD-10 Code Ranges

Complete code families applicable to Fibromuscular Dysplasia

I70-I79Primary Range

Diseases of arteries, arterioles, and capillaries

This range includes codes for various vascular conditions, including fibromuscular dysplasia.

Key Information: ICD-10 code for fibromuscular dysplasia

Essential facts and insights about Fibromuscular Dysplasia

The ICD-10 code for fibromuscular dysplasia is I77.3, used when imaging confirms the characteristic 'string of beads' morphology.

Primary ICD-10-CM Code for fibromuscular dysplasia

Arterial fibromuscular dysplasia
Billable Code

Decision Criteria

clinical Criteria

  • Imaging shows 'string of beads' pattern

documentation Criteria

  • Specific artery involvement documented

coding Criteria

  • Avoid using I77.3 if only 'vascular dysplasia' is documented without arterial specification

Applicable To

  • Multifocal fibromuscular dysplasia
  • Unifocal fibromuscular dysplasia

Excludes

Clinical Validation Requirements

  • Imaging confirms 'string of beads' morphology (CTA/MRA/DSA)
  • Documentation specifies 'multifocal' vs 'unifocal' involvement

Code-Specific Risks

  • Misclassification as atherosclerosis
  • Inadequate documentation of imaging findings

Coding Notes

  • Ensure imaging reports are included in documentation to support FMD diagnosis.

Ancillary Codes

Additional codes that should be used in conjunction with the main diagnosis codes when applicable.

Renal artery stenosis

N28.0
Use when FMD leads to renal artery stenosis.

Essential hypertension

I10
Use when hypertension is secondary to FMD.

Differential Codes

Alternative codes to consider when ruling out similar conditions to the primary diagnosis.

Atherosclerosis of aorta

I70.0
Presence of calcification on imaging differentiates atherosclerosis from FMD.

Hypersensitivity angiitis

M31.0
Elevated CRP/ESR and systemic symptoms indicate vasculitis rather than FMD.

Documentation & Coding Risks

Avoid these common documentation and coding issues when documenting Fibromuscular Dysplasia to ensure proper reimbursement, maintain compliance, and reduce audit risk. These guidelines are particularly important when using ICD-10 code I77.3.

Impact

Clinical: Leads to potential misdiagnosis., Regulatory: Non-compliance with coding standards., Financial: May result in denied claims.

Mitigation Strategy

Require definitive imaging confirmation before coding., Educate staff on documentation standards.

Impact

Reimbursement: Potential underpayment due to missing primary diagnosis code., Compliance: Non-compliance with coding guidelines., Data Quality: Inaccurate representation of patient condition.

Mitigation Strategy

Always pair procedure codes with I77.3.

Impact

Lack of imaging reports to support FMD diagnosis.

Mitigation Strategy

Ensure all imaging findings are documented and accessible.

Documentation errors, coding pitfalls, and audit risks are interconnected aspects of medical coding and billing. Addressing all three areas helps ensure accurate coding, optimal reimbursement, and regulatory compliance.

Frequently Asked Questions

Common questions about ICD-10 coding for Fibromuscular Dysplasia, with expert answers to help guide accurate code selection and documentation.

Documentation Templates for Fibromuscular Dysplasia

Use these documentation templates to ensure complete and accurate documentation for Fibromuscular Dysplasia. These templates include all required elements for proper coding and billing.

Patient with renal artery FMD and hypertension

Specialty: Vascular Surgery

Required Elements

  • Imaging findings
  • Specific artery involvement
  • Complications such as hypertension

Example Documentation

ASSESSMENT: Arterial fibromuscular dysplasia (I77.3) with renal artery involvement. PLAN: Angioplasty scheduled.

Examples: Poor vs. Good Documentation

Poor Documentation Example
Vascular dysplasia noted.
Good Documentation Example
Left renal artery FMD with classic string-of-beads appearance on CTA.
Explanation
The good example provides specific imaging findings and artery involvement.

Need help with ICD-10 coding for Fibromuscular Dysplasia? Ask your questions below.

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