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ICD-10 Coding for Fibrosis(J84.10, J84.112, K74.02, E84.0)

Complete ICD-10-CM coding and documentation guide for Fibrosis. Includes clinical validation requirements, documentation requirements, and coding pitfalls.

Also known as:

ScarringFibrotic Disease

Related ICD-10 Code Ranges

Complete code families applicable to Fibrosis

J84.10-J84.112Primary Range

Pulmonary Fibrosis

Covers unspecified and idiopathic pulmonary fibrosis, critical for respiratory conditions.

Hepatic Fibrosis

Includes unspecified, early, and advanced hepatic fibrosis, important for liver conditions.

Cystic Fibrosis

Encompasses cystic fibrosis with pulmonary and intestinal manifestations.

Code Comparison: When to Use Each Code

Compare key differences between these codes to ensure accurate selection

CodeDescriptionWhen to UseKey Documentation
J84.10Pulmonary fibrosis, unspecifiedUse when the type of pulmonary fibrosis is not specified.
  • Chronic cough
  • Imaging results showing fibrosis
J84.112Idiopathic pulmonary fibrosisUse when idiopathic nature is confirmed by HRCT and biopsy.
  • HRCT showing honeycombing
  • Biopsy confirmation
K74.02Hepatic fibrosis, advancedUse for advanced fibrosis confirmed by biopsy or elastography.
  • Biopsy showing Ishak 5-6
  • Elastography >15 kPa
E84.0Cystic fibrosis with pulmonary manifestationsUse for cystic fibrosis with documented pulmonary involvement.
  • Positive sweat chloride test
  • Genetic confirmation of CFTR mutations

Clinical Decision Support

Always review the patient's clinical documentation thoroughly. When in doubt, choose the more specific code and ensure documentation supports it.

Key Information: ICD-10 code for idiopathic pulmonary fibrosis

Essential facts and insights about Fibrosis

The ICD-10 code for idiopathic pulmonary fibrosis is J84.112, requiring HRCT and biopsy confirmation.

Primary ICD-10-CM Codes for fibrosis

Pulmonary fibrosis, unspecified
Billable Code

Decision Criteria

clinical Criteria

  • No specific type identified

Applicable To

  • Unspecified pulmonary fibrosis

Excludes

  • Idiopathic pulmonary fibrosis (J84.112)

Clinical Validation Requirements

  • Chronic cough
  • Imaging results showing fibrosis

Code-Specific Risks

  • Misclassification if specific type is known

Coding Notes

  • Ensure documentation specifies 'unspecified' if no further details are available.

Ancillary Codes

Additional codes that should be used in conjunction with the main diagnosis codes when applicable.

Pseudomonas infection

B96.5
Use when Pseudomonas is present in cystic fibrosis.

Differential Codes

Alternative codes to consider when ruling out similar conditions to the primary diagnosis.

Idiopathic pulmonary fibrosis

J84.112
Requires HRCT showing honeycombing and exclusion of known causes.

Pulmonary fibrosis, unspecified

J84.10
Use when specific type is not identified.

Hepatic fibrosis, unspecified

K74.00
Use when stage of fibrosis is not specified.

Cystic fibrosis with intestinal manifestations

E84.19
Use when intestinal involvement is primary.

Documentation & Coding Risks

Avoid these common documentation and coding issues when documenting Fibrosis to ensure proper reimbursement, maintain compliance, and reduce audit risk. These guidelines are particularly important when using ICD-10 code J84.10.

Impact

Clinical: May lead to inappropriate treatment plans., Regulatory: Non-compliance with coding standards., Financial: Potential loss of reimbursement.

Mitigation Strategy

Review imaging and biopsy results, Consult with specialists for confirmation

Impact

Reimbursement: Incorrect coding can affect DRG assignment., Compliance: May lead to audit issues., Data Quality: Impacts accuracy of patient records.

Mitigation Strategy

Ensure documentation specifies idiopathic nature for J84.112.

Impact

Reimbursement: Improper sequencing affects reimbursement., Compliance: Non-compliance with coding guidelines., Data Quality: Leads to inaccurate coding data.

Mitigation Strategy

Always code cystic fibrosis first, followed by manifestations.

Impact

High audit risk if documentation does not confirm idiopathic nature.

Mitigation Strategy

Ensure all diagnostic criteria are met and documented.

Documentation errors, coding pitfalls, and audit risks are interconnected aspects of medical coding and billing. Addressing all three areas helps ensure accurate coding, optimal reimbursement, and regulatory compliance.

Frequently Asked Questions

Common questions about ICD-10 coding for Fibrosis, with expert answers to help guide accurate code selection and documentation.

Documentation Templates for Fibrosis

Use these documentation templates to ensure complete and accurate documentation for Fibrosis. These templates include all required elements for proper coding and billing.

Pulmonary Fibrosis Diagnosis

Specialty: Pulmonology

Required Elements

  • HRCT findings
  • Biopsy results
  • Exclusion of known causes

Example Documentation

52yo F with 18mo progressive dyspnea. HRCT shows bilateral basal reticulation with traction bronchiectasis. Surgical biopsy confirms usual interstitial pneumonia pattern. Connective tissue workup negative. Final Dx: Idiopathic pulmonary fibrosis (J84.112).

Examples: Poor vs. Good Documentation

Poor Documentation Example
PF suspected, will monitor
Good Documentation Example
HRCT demonstrates definite UIP pattern per Fleischner criteria. FVC 65% with 8% decline over 6mo. No exposure history. Code: J84.112
Explanation
The good example provides specific imaging findings and excludes other causes, supporting the idiopathic diagnosis.

Need help with ICD-10 coding for Fibrosis? Ask your questions below.

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