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ICD-10 Coding for Focal Segmental Glomerulosclerosis(N04.1)

Complete ICD-10-CM coding and documentation guide for Focal Segmental Glomerulosclerosis. Includes clinical validation requirements, documentation requirements, and coding pitfalls.

Also known as:

FSGSFocal Glomerulosclerosisfocal segmental glomerular lesions

Related ICD-10 Code Ranges

Complete code families applicable to Focal Segmental Glomerulosclerosis

N00-N08Primary Range

Glomerular diseases

This range includes codes for various glomerular diseases, including FSGS.

Key Information: ICD-10 code for FSGS

Essential facts and insights about Focal Segmental Glomerulosclerosis

The ICD-10 code for Focal Segmental Glomerulosclerosis (FSGS) is N04.1.

Primary ICD-10-CM Code for fsgs

Nephrotic syndrome with focal and segmental glomerular lesions
Billable Code

Decision Criteria

clinical Criteria

  • Biopsy shows segmental sclerosis and podocyte effacement.

documentation Criteria

  • Documentation must specify absence of secondary causes.

Applicable To

  • Biopsy-confirmed FSGS lesions
  • Nephrotic syndrome with proteinuria ≥3.5 g/day

Excludes

  • Secondary causes like obesity, diabetes

Clinical Validation Requirements

  • Biopsy showing segmental sclerosis and podocyte effacement
  • Proteinuria ≥3.5 g/day and serum albumin <3.0 g/dL

Code-Specific Risks

  • Misclassification if secondary causes are not ruled out

Coding Notes

  • Ensure documentation specifies primary vs. secondary FSGS.

Ancillary Codes

Additional codes that should be used in conjunction with the main diagnosis codes when applicable.

Type 2 diabetes with diabetic chronic kidney disease

E11.22
Use if FSGS is secondary to diabetes.

Genetic susceptibility to renal disease

Z14.8
Use for familial/genetic FSGS.

Differential Codes

Alternative codes to consider when ruling out similar conditions to the primary diagnosis.

Minimal change disease

N04.0
No segmental sclerosis on biopsy

Documentation & Coding Risks

Avoid these common documentation and coding issues when documenting Focal Segmental Glomerulosclerosis to ensure proper reimbursement, maintain compliance, and reduce audit risk. These guidelines are particularly important when using ICD-10 code N04.1.

Impact

Clinical: Misdiagnosis of FSGS type, Regulatory: Non-compliance with coding standards, Financial: Potential reimbursement issues

Mitigation Strategy

Thoroughly review patient history for secondary causes.

Impact

Reimbursement: Incorrect DRG assignment, Compliance: Non-compliance with ICD-10 rules, Data Quality: Inaccurate clinical data

Mitigation Strategy

Ensure secondary causes are documented and coded first.

Impact

Failure to document secondary causes can lead to audit issues.

Mitigation Strategy

Ensure all potential secondary causes are documented.

Documentation errors, coding pitfalls, and audit risks are interconnected aspects of medical coding and billing. Addressing all three areas helps ensure accurate coding, optimal reimbursement, and regulatory compliance.

Frequently Asked Questions

Common questions about ICD-10 coding for Focal Segmental Glomerulosclerosis, with expert answers to help guide accurate code selection and documentation.

Documentation Templates for Focal Segmental Glomerulosclerosis

Use these documentation templates to ensure complete and accurate documentation for Focal Segmental Glomerulosclerosis. These templates include all required elements for proper coding and billing.

Nephrology Progress Note

Specialty: Nephrology

Required Elements

  • Biopsy findings
  • Proteinuria levels
  • Serum albumin levels

Example Documentation

Assessment: Primary FSGS (N04.1) - Biopsy: Segmental sclerosis, Proteinuria: 4.1g/24h, Serum albumin: 2.7g/dL.

Examples: Poor vs. Good Documentation

Poor Documentation Example
Patient has kidney issues and swelling.
Good Documentation Example
Nephrotic syndrome due to biopsy-confirmed FSGS (N04.1): proteinuria 3.8g/day, serum albumin 2.9g/dL, no diabetic/hypertensive etiology.
Explanation
The good example provides specific clinical details and excludes secondary causes.

Need help with ICD-10 coding for Focal Segmental Glomerulosclerosis? Ask your questions below.

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