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ICD-10 Coding for Hereditary Hemorrhagic Telangiectasia(I78.0)

Complete ICD-10-CM coding and documentation guide for Hereditary Hemorrhagic Telangiectasia. Includes clinical validation requirements, documentation requirements, and coding pitfalls.

Also known as:

Osler-Weber-Rendu SyndromeHHT

Related ICD-10 Code Ranges

Complete code families applicable to Hereditary Hemorrhagic Telangiectasia

I78.0-I78.9Primary Range

Diseases of capillaries

This range includes hereditary hemorrhagic telangiectasia, which is the primary condition being documented.

Key Information: ICD-10 code for hereditary hemorrhagic telangiectasia

Essential facts and insights about Hereditary Hemorrhagic Telangiectasia

The ICD-10 code for hereditary hemorrhagic telangiectasia is I78.0, used when clinical criteria or genetic mutations are confirmed.

Primary ICD-10-CM Code for hereditary hemorrhagic telangiectasia

Hereditary hemorrhagic telangiectasia
Billable Code

Decision Criteria

clinical Criteria

  • Patient meets Curaçao criteria or has genetic confirmation.

Applicable To

  • Osler-Weber-Rendu disease

Excludes

  • Acquired telangiectasia (I78.1)

Clinical Validation Requirements

  • Meets ≥2 Curaçao criteria
  • Genetic testing confirms ENG/ACVRL1/SMAD4 mutation

Code-Specific Risks

  • Coding without sufficient documentation of criteria or genetic confirmation.

Coding Notes

  • Ensure documentation supports the use of I78.0 by including clinical criteria or genetic test results.

Ancillary Codes

Additional codes that should be used in conjunction with the main diagnosis codes when applicable.

Pulmonary arteriovenous malformation

I28.0
Use when imaging confirms a pulmonary AVM.

Differential Codes

Alternative codes to consider when ruling out similar conditions to the primary diagnosis.

Nevus, non-neoplastic

I78.1
Use for acquired telangiectasia without genetic/family history.

Documentation & Coding Risks

Avoid these common documentation and coding issues when documenting Hereditary Hemorrhagic Telangiectasia to ensure proper reimbursement, maintain compliance, and reduce audit risk. These guidelines are particularly important when using ICD-10 code I78.0.

Impact

Clinical: Misdiagnosis risk., Regulatory: Non-compliance with coding guidelines., Financial: Potential claim denials.

Mitigation Strategy

Ensure genetic test results are included in the patient's record.

Impact

Reimbursement: Incorrect coding can lead to denied claims., Compliance: Non-compliance with coding standards., Data Quality: Inaccurate patient records.

Mitigation Strategy

Ensure documentation includes Curaçao criteria or genetic test results.

Impact

Lack of detailed documentation can lead to audit issues.

Mitigation Strategy

Use templates to ensure all criteria are documented.

Documentation errors, coding pitfalls, and audit risks are interconnected aspects of medical coding and billing. Addressing all three areas helps ensure accurate coding, optimal reimbursement, and regulatory compliance.

Frequently Asked Questions

Common questions about ICD-10 coding for Hereditary Hemorrhagic Telangiectasia, with expert answers to help guide accurate code selection and documentation.

Documentation Templates for Hereditary Hemorrhagic Telangiectasia

Use these documentation templates to ensure complete and accurate documentation for Hereditary Hemorrhagic Telangiectasia. These templates include all required elements for proper coding and billing.

Pulmonary AVM in HHT

Specialty: Pulmonology

Required Elements

  • Family history
  • Symptoms
  • Imaging findings
  • Genetic testing

Example Documentation

Patient with HHT presents with symptomatic pulmonary AVM. CT confirms 5mm feeding artery.

Examples: Poor vs. Good Documentation

Poor Documentation Example
Patient has telangiectasia.
Good Documentation Example
Patient has multiple 1-3mm telangiectasia on lips and fingertips, >10 lesions.
Explanation
The good example provides specific details and meets documentation criteria.

Need help with ICD-10 coding for Hereditary Hemorrhagic Telangiectasia? Ask your questions below.

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