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ICD-10 Coding for Idiopathic Pulmonary Hemosiderosis(J84.03)

Complete ICD-10-CM coding and documentation guide for Idiopathic Pulmonary Hemosiderosis. Includes clinical validation requirements, documentation requirements, and coding pitfalls.

Also known as:

IPHPulmonary Hemosiderosis

Related ICD-10 Code Ranges

Complete code families applicable to Idiopathic Pulmonary Hemosiderosis

J84.0-J84.9Primary Range

Other interstitial pulmonary diseases

This range includes idiopathic pulmonary hemosiderosis, which is categorized under other interstitial pulmonary diseases.

Key Information: ICD-10 code for idiopathic pulmonary hemosiderosis

Essential facts and insights about Idiopathic Pulmonary Hemosiderosis

The ICD-10 code for idiopathic pulmonary hemosiderosis is J84.03, used when the condition is confirmed by clinical findings and secondary causes are excluded.

Primary ICD-10-CM Code for idiopathic pulmonary hemosiderosis

Idiopathic pulmonary hemosiderosis
Billable Code

Decision Criteria

clinical Criteria

  • Presence of hemosiderin-laden macrophages in BAL

coding Criteria

  • Exclusion of secondary causes like autoimmune diseases

documentation Criteria

  • Detailed documentation of clinical findings and exclusion criteria

Applicable To

  • Idiopathic pulmonary hemosiderosis

Excludes

  • Pulmonary hemorrhage NOS
  • Autoimmune-related pulmonary hemorrhage

Clinical Validation Requirements

  • Bronchoalveolar lavage showing >40% hemosiderin-laden macrophages
  • HRCT showing diffuse ground-glass opacities
  • Exclusion of vasculitis or autoimmune causes

Code-Specific Risks

  • Misclassification if secondary causes are not excluded
  • Omission of necessary ancillary codes for anemia or respiratory failure

Coding Notes

  • Ensure idiopathic nature is confirmed before using J84.03.

Ancillary Codes

Additional codes that should be used in conjunction with the main diagnosis codes when applicable.

Hemoptysis

R04.2
Use when hemoptysis is present alongside IPH.

Iron-deficiency anemia, unspecified

D50.9
Use when anemia is present due to IPH.

Differential Codes

Alternative codes to consider when ruling out similar conditions to the primary diagnosis.

Lymphoid interstitial pneumonia

J84.2
LIP is characterized by lymphocytic infiltration, not hemosiderin-laden macrophages.

Documentation & Coding Risks

Avoid these common documentation and coding issues when documenting Idiopathic Pulmonary Hemosiderosis to ensure proper reimbursement, maintain compliance, and reduce audit risk. These guidelines are particularly important when using ICD-10 code J84.03.

Impact

Clinical: Leads to misdiagnosis and inappropriate treatment., Regulatory: Non-compliance with documentation standards., Financial: Potential for denied claims due to lack of specificity.

Mitigation Strategy

Ensure thorough clinical evaluation and documentation., Use specific terminology in clinical notes.

Impact

Reimbursement: Incorrect reimbursement due to misclassification., Compliance: Non-compliance with coding guidelines., Data Quality: Inaccurate data affecting clinical research and statistics.

Mitigation Strategy

Require biopsy confirmation and exclusion of secondary causes.

Impact

High risk of audit if secondary causes are not excluded.

Mitigation Strategy

Require biopsy and BAL confirmation in documentation.

Documentation errors, coding pitfalls, and audit risks are interconnected aspects of medical coding and billing. Addressing all three areas helps ensure accurate coding, optimal reimbursement, and regulatory compliance.

Frequently Asked Questions

Common questions about ICD-10 coding for Idiopathic Pulmonary Hemosiderosis, with expert answers to help guide accurate code selection and documentation.

Documentation Templates for Idiopathic Pulmonary Hemosiderosis

Use these documentation templates to ensure complete and accurate documentation for Idiopathic Pulmonary Hemosiderosis. These templates include all required elements for proper coding and billing.

Acute episode of idiopathic pulmonary hemosiderosis

Specialty: Pulmonology

Required Elements

  • Presenting symptoms
  • Laboratory findings
  • Imaging results
  • Biopsy results
  • Treatment plan

Example Documentation

Assessment: Idiopathic pulmonary hemosiderosis (J84.03). Findings: BAL: 90% hemosiderin-laden macrophages. HRCT: Bilateral ground-glass opacities. Labs: Hgb 7.8 g/dL, ferritin 12 ng/mL. Plan: Prednisone 1 mg/kg/day.

Examples: Poor vs. Good Documentation

Poor Documentation Example
Pulmonary hemorrhage with anemia.
Good Documentation Example
Idiopathic pulmonary hemosiderosis confirmed by BAL showing >40% hemosiderin-laden macrophages and exclusion of vasculitis.
Explanation
The good example provides specific diagnostic criteria and excludes other causes, ensuring accurate coding.

Need help with ICD-10 coding for Idiopathic Pulmonary Hemosiderosis? Ask your questions below.

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