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ICD-10 Coding for Kawasaki Disease(M30.3)

Complete ICD-10-CM coding and documentation guide for Kawasaki Disease. Includes clinical validation requirements, documentation requirements, and coding pitfalls.

Also known as:

Mucocutaneous Lymph Node Syndrome

Related ICD-10 Code Ranges

Complete code families applicable to Kawasaki Disease

M30-M36Primary Range

Systemic connective tissue disorders

This range includes Kawasaki disease, which is a systemic vasculitis.

Key Information: ICD-10 code for Kawasaki disease

Essential facts and insights about Kawasaki Disease

The ICD-10 code for Kawasaki disease is M30.3, used for confirmed cases meeting diagnostic criteria.

Primary ICD-10-CM Code for kawasaki disease

Mucocutaneous lymph node syndrome [Kawasaki]
Billable Code

Decision Criteria

clinical Criteria

  • Presence of fever for ≥5 days and 4/5 principal clinical features.

documentation Criteria

  • Documented echocardiogram findings of coronary artery changes.

Applicable To

  • Classic Kawasaki disease
  • Incomplete Kawasaki disease

Excludes

Clinical Validation Requirements

  • Fever for ≥5 days
  • Presence of at least 4 of 5 principal clinical features
  • Elevated CRP or ESR
  • Coronary artery abnormalities on echocardiogram

Code-Specific Risks

  • Incorrect use without meeting full diagnostic criteria
  • Failure to document all required clinical features

Coding Notes

  • Ensure all clinical criteria are documented before coding M30.3.

Ancillary Codes

Additional codes that should be used in conjunction with the main diagnosis codes when applicable.

Coronary artery aneurysm

I25.41
Use when echocardiogram shows coronary artery aneurysm.

Prolonged fever

R50.9
Use for fever lasting ≥5 days as a symptom of Kawasaki disease.

Differential Codes

Alternative codes to consider when ruling out similar conditions to the primary diagnosis.

Toxic shock syndrome

A48.4
Presence of hypotension and multi-organ involvement without coronary changes.

Scarlet fever

A38.9
Presence of sandpaper rash and positive strep culture.

Documentation & Coding Risks

Avoid these common documentation and coding issues when documenting Kawasaki Disease to ensure proper reimbursement, maintain compliance, and reduce audit risk. These guidelines are particularly important when using ICD-10 code M30.3.

Impact

Clinical: Misdiagnosis or delayed treatment., Regulatory: Non-compliance with coding standards., Financial: Potential claim denials.

Mitigation Strategy

Use checklists for clinical criteria., Regular training on documentation standards.

Impact

Reimbursement: Incorrect coding can lead to denied claims., Compliance: Non-compliance with ICD-10 guidelines., Data Quality: Inaccurate clinical data affecting patient records.

Mitigation Strategy

Ensure all clinical features and lab results are documented.

Impact

Incomplete documentation of clinical criteria for Kawasaki disease.

Mitigation Strategy

Implement regular audits and training sessions.

Documentation errors, coding pitfalls, and audit risks are interconnected aspects of medical coding and billing. Addressing all three areas helps ensure accurate coding, optimal reimbursement, and regulatory compliance.

Frequently Asked Questions

Common questions about ICD-10 coding for Kawasaki Disease, with expert answers to help guide accurate code selection and documentation.

Documentation Templates for Kawasaki Disease

Use these documentation templates to ensure complete and accurate documentation for Kawasaki Disease. These templates include all required elements for proper coding and billing.

Initial diagnosis of Kawasaki Disease

Specialty: Pediatrics

Required Elements

  • Fever duration
  • Principal clinical features
  • Laboratory findings
  • Echocardiogram results

Example Documentation

Patient presents with fever for 6 days, conjunctivitis, rash, and coronary artery changes on echo.

Examples: Poor vs. Good Documentation

Poor Documentation Example
Fever and rash noted.
Good Documentation Example
Fever for 6 days, conjunctivitis, rash, and coronary artery aneurysm on echo.
Explanation
The good example includes all necessary clinical features and diagnostic findings.

Need help with ICD-10 coding for Kawasaki Disease? Ask your questions below.

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