Back to HomeBeta

ICD-10 Coding for Myelodysplastic Syndrome(D46.0, D46.1, D46.9)

Complete ICD-10-CM coding and documentation guide for Myelodysplastic Syndrome. Includes clinical validation requirements, documentation requirements, and coding pitfalls.

Also known as:

MDSPreleukemia

Related ICD-10 Code Ranges

Complete code families applicable to Myelodysplastic Syndrome

D46Primary Range

Myelodysplastic syndromes

This range includes all specific types of myelodysplastic syndromes, which are disorders caused by poorly formed or dysfunctional blood cells.

Code Comparison: When to Use Each Code

Compare key differences between these codes to ensure accurate selection

CodeDescriptionWhen to UseKey Documentation
D46.0Refractory anemia without ring sideroblasts, so statedUse when refractory anemia is diagnosed without the presence of ring sideroblasts.
  • Bone marrow biopsy showing dysplasia in ≥10% of cells in one or more myeloid cell lines
  • Absence of ring sideroblasts
D46.1Refractory anemia with ring sideroblastsUse when refractory anemia is diagnosed with the presence of ring sideroblasts.
  • Bone marrow biopsy showing ≥15% ring sideroblasts
  • SF3B1 mutation may be present
D46.9Myelodysplastic syndrome, unspecifiedUse when MDS is diagnosed but specific subtype is not documented.
  • General diagnosis of MDS without specific subtype identified

Clinical Decision Support

Always review the patient's clinical documentation thoroughly. When in doubt, choose the more specific code and ensure documentation supports it.

Key Information: ICD-10 code for myelodysplastic syndrome

Essential facts and insights about Myelodysplastic Syndrome

The ICD-10 code for myelodysplastic syndrome is D46, with specific subtypes like D46.0 and D46.1.

Primary ICD-10-CM Codes for myelodysplastic syndrome

Refractory anemia without ring sideroblasts, so stated
Billable Code

Decision Criteria

clinical Criteria

  • Absence of ring sideroblasts confirmed by bone marrow biopsy.

Applicable To

  • Refractory anemia without ring sideroblasts

Excludes

  • Refractory anemia with ring sideroblasts (D46.1)

Clinical Validation Requirements

  • Bone marrow biopsy showing dysplasia in ≥10% of cells in one or more myeloid cell lines
  • Absence of ring sideroblasts

Code-Specific Risks

  • Misclassification if ring sideroblasts are present but not documented.

Coding Notes

  • Ensure documentation specifies absence of ring sideroblasts.

Differential Codes

Alternative codes to consider when ruling out similar conditions to the primary diagnosis.

Refractory anemia with ring sideroblasts

D46.1
Presence of ≥15% ring sideroblasts in bone marrow.

Refractory anemia without ring sideroblasts

D46.0
Absence of ring sideroblasts in bone marrow.

Documentation & Coding Risks

Avoid these common documentation and coding issues when documenting Myelodysplastic Syndrome to ensure proper reimbursement, maintain compliance, and reduce audit risk. These guidelines are particularly important when using ICD-10 code D46.0.

Impact

Clinical: May lead to inappropriate treatment plans., Regulatory: Increases risk of audit and compliance issues., Financial: Potential for reduced reimbursement.

Mitigation Strategy

Educate clinicians on the importance of detailed documentation., Implement checklists for documentation requirements.

Impact

Reimbursement: May result in lower reimbursement rates., Compliance: Increases risk of audit due to lack of specificity., Data Quality: Reduces accuracy of clinical data.

Mitigation Strategy

Ensure documentation specifies the subtype of MDS for accurate coding.

Impact

High audit risk when using D46.9 without specific subtype documentation.

Mitigation Strategy

Encourage detailed documentation and use of specific codes.

Documentation errors, coding pitfalls, and audit risks are interconnected aspects of medical coding and billing. Addressing all three areas helps ensure accurate coding, optimal reimbursement, and regulatory compliance.

Frequently Asked Questions

Common questions about ICD-10 coding for Myelodysplastic Syndrome, with expert answers to help guide accurate code selection and documentation.

Documentation Templates for Myelodysplastic Syndrome

Use these documentation templates to ensure complete and accurate documentation for Myelodysplastic Syndrome. These templates include all required elements for proper coding and billing.

Refractory anemia with ring sideroblasts

Specialty: Hematology

Required Elements

  • Bone marrow biopsy results
  • Presence of ring sideroblasts
  • Genetic mutation analysis

Example Documentation

Patient presents with refractory anemia. Bone marrow biopsy shows 18% ring sideroblasts. SF3B1 mutation confirmed.

Examples: Poor vs. Good Documentation

Poor Documentation Example
MDS, stable
Good Documentation Example
RAEB-2 (D46.22): 14% blasts on 3/24/25 BM biopsy, complex karyotype including -7/del(7q), transfusion-dependent anemia (Hgb 7.2 g/dL)
Explanation
The good example provides specific details on blast percentage, karyotype, and transfusion dependence, which are necessary for accurate coding.

Need help with ICD-10 coding for Myelodysplastic Syndrome? Ask your questions below.

Ask about any ICD-10 CM code, or paste a medical note

We build tools for
clinician happiness.

Learn More at Freed.ai
Back to HomeBeta

Built by Freed

Try Freed for free for 7 days.

Learn more