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ICD-10 Coding for Myotonic Dystrophy(G71.11, G71.19)

Complete ICD-10-CM coding and documentation guide for Myotonic Dystrophy. Includes clinical validation requirements, documentation requirements, and coding pitfalls.

Also known as:

DM1DM2Steinert's Disease

Related ICD-10 Code Ranges

Complete code families applicable to Myotonic Dystrophy

G71.1Primary Range

Muscular dystrophies

This range includes specific codes for myotonic dystrophy types 1 and 2, which are the primary focus for coding this condition.

Code Comparison: When to Use Each Code

Compare key differences between these codes to ensure accurate selection

CodeDescriptionWhen to UseKey Documentation
G71.11Myotonic muscular dystrophyUse for patients with confirmed DM1 through genetic testing and clinical presentation.
  • Confirmed DMPK CTG repeat expansion (≥50 repeats)
  • Clinical myotonia and multisystem involvement
G71.19Other myotonic disordersUse for patients with confirmed DM2 through genetic testing.
  • Confirmed CNBP CCTG repeat expansion
  • Proximal muscle weakness without severe congenital forms

Clinical Decision Support

Always review the patient's clinical documentation thoroughly. When in doubt, choose the more specific code and ensure documentation supports it.

Key Information: ICD-10 code for myotonic dystrophy

Essential facts and insights about Myotonic Dystrophy

The ICD-10 code for myotonic dystrophy type 1 is G71.11, and for type 2, it is G71.19.

Primary ICD-10-CM Codes for myotonic dystrophy

Myotonic muscular dystrophy
Billable Code

Decision Criteria

clinical Criteria

  • Presence of CTG repeat expansion in DMPK gene

documentation Criteria

  • Detailed documentation of clinical manifestations and genetic testing

Applicable To

  • Myotonic dystrophy type 1 (DM1)

Excludes

  • Other myotonic disorders

Clinical Validation Requirements

  • Confirmed DMPK CTG repeat expansion (≥50 repeats)
  • Clinical myotonia and multisystem involvement

Code-Specific Risks

  • Confusion with diabetes mellitus if abbreviated as DM without clarification.

Coding Notes

  • Ensure genetic testing results are documented to support the use of this code.

Ancillary Codes

Additional codes that should be used in conjunction with the main diagnosis codes when applicable.

Muscle contracture, unspecified

M62.40
Use to specify muscle contractures associated with myotonic dystrophy.

Contracture of joint, unspecified

M24.50
Use to specify joint contractures associated with myotonic dystrophy.

Differential Codes

Alternative codes to consider when ruling out similar conditions to the primary diagnosis.

Other myotonic disorders

G71.19
Use for DM2 or other myotonic disorders not classified as DM1.

Myotonic muscular dystrophy

G71.11
Use for DM1 with specific genetic and clinical criteria.

Documentation & Coding Risks

Avoid these common documentation and coding issues when documenting Myotonic Dystrophy to ensure proper reimbursement, maintain compliance, and reduce audit risk. These guidelines are particularly important when using ICD-10 code G71.11.

Impact

Clinical: Leads to inappropriate treatment plans., Regulatory: Non-compliance with coding guidelines., Financial: Potential for denied claims or incorrect billing.

Mitigation Strategy

Always specify DM1 or DM2 in documentation., Ensure genetic testing is performed and documented.

Impact

Reimbursement: Incorrect coding can lead to denied claims or incorrect reimbursement., Compliance: Non-compliance with coding standards and potential audit issues., Data Quality: Impacts the accuracy of patient records and data analysis.

Mitigation Strategy

Always specify 'DM1' or 'DM2' to avoid confusion with diabetes mellitus.

Impact

Lack of genetic test documentation can lead to audit failures.

Mitigation Strategy

Ensure all genetic testing results are included in patient records.

Documentation errors, coding pitfalls, and audit risks are interconnected aspects of medical coding and billing. Addressing all three areas helps ensure accurate coding, optimal reimbursement, and regulatory compliance.

Frequently Asked Questions

Common questions about ICD-10 coding for Myotonic Dystrophy, with expert answers to help guide accurate code selection and documentation.

Documentation Templates for Myotonic Dystrophy

Use these documentation templates to ensure complete and accurate documentation for Myotonic Dystrophy. These templates include all required elements for proper coding and billing.

Neurology Progress Note for DM1

Specialty: Neurology

Required Elements

  • Genetic test results
  • Clinical manifestations
  • Functional status
  • Cardiac evaluation

Example Documentation

Assessment: Myotonic dystrophy type 1 (G71.11) confirmed by CTG repeat expansion. Current manifestations include grip myotonia and dysphagia.

Examples: Poor vs. Good Documentation

Poor Documentation Example
DM with weakness and heart problems
Good Documentation Example
G71.11: DM1 with CTG repeat n=820. Bilateral ptosis, proximal > distal weakness (MRC 4/5). 24-hour Holter shows sinus pauses >3s. Dysphagia managed with thickened liquids.
Explanation
The good example provides specific genetic and clinical details, improving clarity and coding accuracy.

Need help with ICD-10 coding for Myotonic Dystrophy? Ask your questions below.

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