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ICD-10 Coding for Polycythaemia(D45, D75.0, D75.1)

Complete ICD-10-CM coding and documentation guide for Polycythaemia. Includes clinical validation requirements, documentation requirements, and coding pitfalls.

Also known as:

Polycythemia veraSecondary polycythemiaFamilial erythrocytosis

Related ICD-10 Code Ranges

Complete code families applicable to Polycythaemia

D45-D47Primary Range

Myeloproliferative diseases

This range includes primary codes for polycythemia vera and related myeloproliferative disorders.

Other and unspecified diseases of blood and blood-forming organs

This range includes codes for secondary and familial polycythemia.

Code Comparison: When to Use Each Code

Compare key differences between these codes to ensure accurate selection

CodeDescriptionWhen to UseKey Documentation
D45Polycythemia veraUse when polycythemia vera is confirmed by WHO criteria.
  • JAK2 mutation
  • Elevated hematocrit/hemoglobin
  • Bone marrow biopsy showing trilineage hyperplasia
D75.0Familial erythrocytosisUse when familial erythrocytosis is confirmed by genetic testing.
  • EPOR mutation
  • Normal EPO levels
  • Family history
D75.1Secondary polycythemiaUse when polycythemia is due to secondary causes.
  • History of smoking, COPD, or high-altitude living
  • Normal or elevated EPO levels

Clinical Decision Support

Always review the patient's clinical documentation thoroughly. When in doubt, choose the more specific code and ensure documentation supports it.

Key Information: ICD-10 code for polycythemia vera

Essential facts and insights about Polycythaemia

The ICD-10 code for polycythemia vera is D45, used when confirmed by WHO criteria.

Primary ICD-10-CM Codes for polycythaemia

Polycythemia vera
Billable Code

Decision Criteria

clinical Criteria

  • JAK2 mutation and elevated hematocrit

documentation Criteria

  • Bone marrow biopsy showing trilineage hyperplasia

Applicable To

  • Primary polycythemia

Excludes

  • Familial polycythemia (D75.0)
  • Secondary polycythemia (D75.1)

Clinical Validation Requirements

  • JAK2 mutation
  • Elevated hematocrit/hemoglobin
  • Bone marrow biopsy showing trilineage hyperplasia

Code-Specific Risks

  • Misclassification if JAK2 mutation is not confirmed

Coding Notes

  • Ensure documentation includes JAK2 status and bone marrow findings.

Differential Codes

Alternative codes to consider when ruling out similar conditions to the primary diagnosis.

Familial erythrocytosis

D75.0
Presence of EPOR mutation and family history.

Secondary polycythemia

D75.1
Presence of secondary causes like smoking or high-altitude living.

Polycythemia vera

D45
JAK2 mutation and bone marrow findings.

Documentation & Coding Risks

Avoid these common documentation and coding issues when documenting Polycythaemia to ensure proper reimbursement, maintain compliance, and reduce audit risk. These guidelines are particularly important when using ICD-10 code D45.

Impact

Clinical: Misdiagnosis of polycythemia type., Regulatory: Non-compliance with coding guidelines., Financial: Potential for incorrect billing and reimbursement.

Mitigation Strategy

Thorough patient history review, Document all potential secondary causes

Impact

Reimbursement: Incorrect DRG assignment may occur., Compliance: Potential for audit and recoupment., Data Quality: Inaccurate data on polycythemia prevalence.

Mitigation Strategy

Query provider for clarification or use D75.1 if secondary causes are suspected.

Impact

High risk of audit if D45 is used without documented JAK2 mutation.

Mitigation Strategy

Ensure JAK2 mutation is documented before coding D45.

Documentation errors, coding pitfalls, and audit risks are interconnected aspects of medical coding and billing. Addressing all three areas helps ensure accurate coding, optimal reimbursement, and regulatory compliance.

Frequently Asked Questions

Common questions about ICD-10 coding for Polycythaemia, with expert answers to help guide accurate code selection and documentation.

Documentation Templates for Polycythaemia

Use these documentation templates to ensure complete and accurate documentation for Polycythaemia. These templates include all required elements for proper coding and billing.

Hematology consult for suspected polycythemia

Specialty: Hematology

Required Elements

  • JAK2 mutation status
  • Hematocrit levels
  • Bone marrow biopsy findings
  • EPO levels

Examples: Poor vs. Good Documentation

Poor Documentation Example
Elevated RBC count, possible PV
Good Documentation Example
68M with JAK2 V617F+, Hct 52%, hypercellular marrow with panmyelosis, EPO 3.2 mU/mL. Meets WHO criteria for PV.
Explanation
The good example provides specific clinical criteria and test results confirming the diagnosis.

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