ICD-10 Coding for Primary Myelofibrosis(D47.4, D75.81)
Complete ICD-10-CM coding and documentation guide for Primary Myelofibrosis. Includes clinical validation requirements, documentation requirements, and coding pitfalls.
Also known as:
Related ICD-10 Code Ranges
Complete code families applicable to Primary Myelofibrosis
D47-D47.9Primary Range
Other neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue
This range includes codes for chronic myeloproliferative diseases, including primary myelofibrosis.
Other and unspecified diseases of blood and blood-forming organs
This range includes codes for secondary myelofibrosis and other related conditions.
Code Comparison: When to Use Each Code
Compare key differences between these codes to ensure accurate selection
| Code | Description | When to Use | Key Documentation |
|---|---|---|---|
| D47.4 | Osteomyelofibrosis | Use for confirmed cases of primary myelofibrosis with appropriate clinical documentation. |
|
| D75.81 | Myelofibrosis | Use for secondary myelofibrosis or when primary status is not specified. |
|
Clinical Decision Support
Always review the patient's clinical documentation thoroughly. When in doubt, choose the more specific code and ensure documentation supports it.
Key Information: ICD-10 code for primary myelofibrosis
Essential facts and insights about Primary Myelofibrosis
Primary ICD-10-CM Codes for primary myelofibrosis
Decision Criteria
clinical Criteria
- Presence of JAK2, CALR, or MPL mutations
documentation Criteria
- Bone marrow biopsy showing fibrosis grade ≥2
coding Criteria
- Exclusion of other myeloid neoplasms
Applicable To
- Chronic idiopathic myelofibrosis
- Primary myelofibrosis
Excludes
- Acute myelofibrosis (C94.4)
Clinical Validation Requirements
- Bone marrow biopsy showing fibrosis grade ≥2
- Presence of JAK2, CALR, or MPL mutations
- Exclusion of other myeloid neoplasms
Code-Specific Risks
- Misclassification as secondary myelofibrosis
- Lack of specific mutation documentation
Coding Notes
- Ensure documentation specifies 'primary' or 'idiopathic' to use D47.4.
D75.81 - Myelofibrosis
Use for secondary myelofibrosis or when primary status is not specified.
Applicable To
- Secondary myelofibrosis NOS
Clinical Validation Requirements
- Documentation of secondary cause or unspecified myelofibrosis
Coding Notes
Ensure secondary cause is documented if applicable.
Ancillary Codes
Additional codes that should be used in conjunction with the main diagnosis codes when applicable.
Documentation & Coding Risks
Avoid these common documentation and coding issues when documenting Primary Myelofibrosis to ensure proper reimbursement, maintain compliance, and reduce audit risk. These guidelines are particularly important when using ICD-10 code D47.4.
Impact
Clinical: Leads to potential misclassification of the condition., Regulatory: Non-compliance with coding specificity requirements., Financial: May affect reimbursement due to incorrect DRG assignment.
Mitigation Strategy
Always specify 'primary' or 'secondary' in documentation., Query provider if documentation is unclear.
Impact
Reimbursement: Incorrect DRG assignment leading to reimbursement issues., Compliance: Non-compliance with coding guidelines., Data Quality: Inaccurate clinical data representation.
Mitigation Strategy
Query provider to confirm 'primary' vs. 'secondary' etiology.
Impact
Using D75.81 for primary myelofibrosis cases.
Mitigation Strategy
Implement regular training on distinguishing primary vs. secondary myelofibrosis.
Documentation errors, coding pitfalls, and audit risks are interconnected aspects of medical coding and billing. Addressing all three areas helps ensure accurate coding, optimal reimbursement, and regulatory compliance.
Frequently Asked Questions
Common questions about ICD-10 coding for Primary Myelofibrosis, with expert answers to help guide accurate code selection and documentation.
Documentation Templates for Primary Myelofibrosis
Use these documentation templates to ensure complete and accurate documentation for Primary Myelofibrosis. These templates include all required elements for proper coding and billing.
Primary Myelofibrosis Diagnosis
Specialty: HematologyRequired Elements
- Bone marrow biopsy findings
- Mutation status
- Splenomegaly assessment
Example Documentation
Examples: Poor vs. Good Documentation
Poor Documentation Example
Good Documentation Example
Explanation
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