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ICD-10 Coding for Sarcoidosis(D86.0, D86.3, D86.81)

Complete ICD-10-CM coding and documentation guide for Sarcoidosis. Includes clinical validation requirements, documentation requirements, and coding pitfalls.

Also known as:

Besnier-Boeck diseaseBoeck's sarcoid

Related ICD-10 Code Ranges

Complete code families applicable to Sarcoidosis

D86.0-D86.9Primary Range

Sarcoidosis

This range includes all codes related to sarcoidosis, specifying different organ involvements.

Code Comparison: When to Use Each Code

Compare key differences between these codes to ensure accurate selection

CodeDescriptionWhen to UseKey Documentation
D86.0Sarcoidosis of lungUse when sarcoidosis is confirmed in the lungs with appropriate clinical validation.
  • Histopathology report showing non-caseating granulomas
  • Chest imaging showing bilateral hilar lymphadenopathy
D86.3Sarcoidosis of skinUse when sarcoidosis is confirmed in the skin with biopsy evidence.
  • Skin biopsy showing non-caseating granulomas
D86.81Sarcoid meningitisUse when sarcoidosis involves the meninges with clinical and imaging confirmation.
  • CSF analysis showing lymphocytic pleocytosis
  • MRI showing meningeal enhancement

Clinical Decision Support

Always review the patient's clinical documentation thoroughly. When in doubt, choose the more specific code and ensure documentation supports it.

Key Information: ICD-10 code for sarcoidosis

Essential facts and insights about Sarcoidosis

The ICD-10 code for sarcoidosis of the lung is D86.0, used when confirmed with clinical validation.

Primary ICD-10-CM Codes for sarcoidosis

Sarcoidosis of lung
Billable Code

Decision Criteria

clinical Criteria

  • Non-caseating granulomas on lung biopsy

documentation Criteria

  • Exclusion of tuberculosis

Applicable To

  • Pulmonary sarcoidosis

Excludes

  • Tuberculosis of lung (A15.0)

Clinical Validation Requirements

  • Histopathology report showing non-caseating granulomas
  • Chest imaging showing bilateral hilar lymphadenopathy

Code-Specific Risks

  • Risk of misclassification if TB is not excluded

Coding Notes

  • Ensure TB is ruled out before using this code.

Differential Codes

Alternative codes to consider when ruling out similar conditions to the primary diagnosis.

Tuberculosis of lung

A15.0
Presence of caseating granulomas and positive TB test

Lupus vulgaris

A18.4
Presence of caseating granulomas and positive TB test

Meningitis, unspecified

G03.9
Lack of specific sarcoidosis confirmation

Documentation & Coding Risks

Avoid these common documentation and coding issues when documenting Sarcoidosis to ensure proper reimbursement, maintain compliance, and reduce audit risk. These guidelines are particularly important when using ICD-10 code D86.0.

Impact

Clinical: Misdiagnosis risk, Regulatory: Non-compliance with coding standards, Financial: Potential claim denials

Mitigation Strategy

Always include TB test results, Ensure differential diagnosis is documented

Impact

Reimbursement: Lower reimbursement due to unspecified codes, Compliance: Increased audit risk, Data Quality: Decreased accuracy in clinical data

Mitigation Strategy

Always specify the organ involved and use the corresponding specific code.

Impact

High audit risk when specific organ involvement is not documented

Mitigation Strategy

Ensure documentation specifies the organ involved and use the corresponding specific code.

Documentation errors, coding pitfalls, and audit risks are interconnected aspects of medical coding and billing. Addressing all three areas helps ensure accurate coding, optimal reimbursement, and regulatory compliance.

Frequently Asked Questions

Common questions about ICD-10 coding for Sarcoidosis, with expert answers to help guide accurate code selection and documentation.

Documentation Templates for Sarcoidosis

Use these documentation templates to ensure complete and accurate documentation for Sarcoidosis. These templates include all required elements for proper coding and billing.

Pulmonary Sarcoidosis

Specialty: Pulmonology

Required Elements

  • Biopsy results
  • Imaging findings
  • Exclusion of TB

Example Documentation

Patient presents with cough and dyspnea. Biopsy confirms non-caseating granulomas. Imaging shows bilateral hilar lymphadenopathy. TB excluded.

Examples: Poor vs. Good Documentation

Poor Documentation Example
Patient has sarcoidosis.
Good Documentation Example
Patient diagnosed with pulmonary sarcoidosis. Biopsy confirms non-caseating granulomas. Imaging shows bilateral hilar lymphadenopathy. TB excluded.
Explanation
The good example provides specific organ involvement and clinical validation.

Need help with ICD-10 coding for Sarcoidosis? Ask your questions below.

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