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ICD-10 Coding for Usual Interstitial Pneumonitis(J84.178)

Complete ICD-10-CM coding and documentation guide for Usual Interstitial Pneumonitis. Includes clinical validation requirements, documentation requirements, and coding pitfalls.

Also known as:

Usual Interstitial PneumoniaUIP

Related ICD-10 Code Ranges

Complete code families applicable to Usual Interstitial Pneumonitis

J84.1Primary Range

Other interstitial pulmonary diseases with fibrosis

This range includes conditions like UIP and other fibrotic interstitial lung diseases.

Interstitial pulmonary disease, unspecified

Used when specific interstitial lung disease cannot be confirmed.

Key Information: ICD-10 code for usual interstitial pneumonitis

Essential facts and insights about Usual Interstitial Pneumonitis

The ICD-10 code for usual interstitial pneumonitis is J84.178, used when UIP is confirmed through HRCT and multidisciplinary consensus.

Primary ICD-10-CM Code for usual interstitial pneumonitis

Usual interstitial pneumonia
Billable Code

Decision Criteria

clinical Criteria

  • HRCT findings consistent with UIP pattern

documentation Criteria

  • Multidisciplinary consensus documented

Applicable To

  • Idiopathic pulmonary fibrosis with UIP pattern

Excludes

  • Hypersensitivity pneumonitis
  • Non-specific interstitial pneumonia

Clinical Validation Requirements

  • HRCT showing subpleural, basal-predominant reticulation with honeycombing
  • Multidisciplinary diagnosis excluding known causes
  • Histopathology confirming temporal heterogeneity with fibroblastic foci

Code-Specific Risks

  • Incorrectly coding unspecified interstitial lung disease
  • Missing documentation of HRCT findings

Coding Notes

  • Ensure HRCT and multidisciplinary consensus are documented.

Ancillary Codes

Additional codes that should be used in conjunction with the main diagnosis codes when applicable.

Connective tissue disease, unspecified

M35.9
Use when UIP is secondary to a connective tissue disease.

Differential Codes

Alternative codes to consider when ruling out similar conditions to the primary diagnosis.

Other interstitial pulmonary diseases with fibrosis

J84.1
Used for other fibrotic interstitial lung diseases not specifically UIP.

Interstitial pulmonary disease, unspecified

J84.9
Used when specific interstitial lung disease cannot be confirmed.

Documentation & Coding Risks

Avoid these common documentation and coding issues when documenting Usual Interstitial Pneumonitis to ensure proper reimbursement, maintain compliance, and reduce audit risk. These guidelines are particularly important when using ICD-10 code J84.178.

Impact

Clinical: Potential misdiagnosis, Regulatory: Non-compliance with coding standards, Financial: Reduced reimbursement

Mitigation Strategy

Ensure specific terminology is used, Educate clinicians on documentation standards

Impact

Reimbursement: Lower reimbursement due to unspecified coding, Compliance: Non-compliance with coding guidelines, Data Quality: Decreased accuracy in clinical data

Mitigation Strategy

Require 'UIP pattern' or 'multidisciplinary confirmation' in notes

Impact

Lack of specific HRCT documentation can lead to audit issues.

Mitigation Strategy

Ensure all HRCT findings are clearly documented in the patient record.

Documentation errors, coding pitfalls, and audit risks are interconnected aspects of medical coding and billing. Addressing all three areas helps ensure accurate coding, optimal reimbursement, and regulatory compliance.

Frequently Asked Questions

Common questions about ICD-10 coding for Usual Interstitial Pneumonitis, with expert answers to help guide accurate code selection and documentation.

Documentation Templates for Usual Interstitial Pneumonitis

Use these documentation templates to ensure complete and accurate documentation for Usual Interstitial Pneumonitis. These templates include all required elements for proper coding and billing.

Confirmed UIP with HRCT and Multidisciplinary Consensus

Specialty: Pulmonology

Required Elements

  • HRCT findings
  • Multidisciplinary consensus
  • Exclusion of other causes

Example Documentation

68M with progressive dyspnea. HRCT shows subpleural reticulation, traction bronchiectasis, and honeycombing in lower lobes. No CTD/occupational exposure. MDD confirms idiopathic UIP.

Examples: Poor vs. Good Documentation

Poor Documentation Example
Patient has interstitial lung disease.
Good Documentation Example
HRCT shows basal-predominant honeycombing consistent with UIP pattern. Multidisciplinary consensus confirms idiopathic UIP.
Explanation
The good example provides specific HRCT findings and multidisciplinary confirmation, ensuring accurate coding.

Need help with ICD-10 coding for Usual Interstitial Pneumonitis? Ask your questions below.

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