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ICD-10 Coding for Waldenström's Macroglobulinemia(C88.00, C88.01)

Complete ICD-10-CM coding and documentation guide for Waldenström's Macroglobulinemia. Includes clinical validation requirements, documentation requirements, and coding pitfalls.

Also known as:

WMLymphoplasmacytic Lymphoma with IgM Production

Related ICD-10 Code Ranges

Complete code families applicable to Waldenström's Macroglobulinemia

C88.0-C88.9Primary Range

Malignant immunoproliferative diseases

This range includes codes for Waldenström's macroglobulinemia and related immunoproliferative disorders.

Code Comparison: When to Use Each Code

Compare key differences between these codes to ensure accurate selection

CodeDescriptionWhen to UseKey Documentation
C88.00Waldenström's macroglobulinemia without complicationsUse when WM is confirmed without any complications.
  • Bone marrow biopsy showing ≥10% lymphoplasmacytic infiltration
  • MYD88 L265P mutation detected by PCR
C88.01Waldenström's macroglobulinemia with refractory/relapsed diseaseUse when WM is refractory or relapsed after treatment.
  • Progression after 2+ lines of therapy
  • Documented resistance to treatments like ibrutinib

Clinical Decision Support

Always review the patient's clinical documentation thoroughly. When in doubt, choose the more specific code and ensure documentation supports it.

Key Information: ICD-10 code for Waldenström's macroglobulinemia

Essential facts and insights about Waldenström's Macroglobulinemia

The ICD-10 code for Waldenström's macroglobulinemia is C88.00 for cases without complications and C88.01 for refractory or relapsed disease.

Primary ICD-10-CM Codes for waldenstrom's

Waldenström's macroglobulinemia without complications
Billable Code

Decision Criteria

clinical Criteria

  • Confirmed diagnosis of WM with bone marrow biopsy and MYD88 mutation.

Applicable To

  • Asymptomatic Waldenström's macroglobulinemia

Excludes

  • Small cell B-cell lymphoma (C83.0)

Clinical Validation Requirements

  • Bone marrow biopsy showing ≥10% lymphoplasmacytic infiltration
  • MYD88 L265P mutation detected by PCR

Code-Specific Risks

  • Misclassification with other lymphomas due to similar symptoms.

Coding Notes

  • Ensure documentation explicitly states Waldenström's macroglobulinemia.

Ancillary Codes

Additional codes that should be used in conjunction with the main diagnosis codes when applicable.

Hyperviscosity syndrome

R70.1
Use when hyperviscosity symptoms are present with WM.

Differential Codes

Alternative codes to consider when ruling out similar conditions to the primary diagnosis.

Small cell B-cell lymphoma

C83.0
Presence of CD5+/CD10+ expression differentiates it from WM.

Documentation & Coding Risks

Avoid these common documentation and coding issues when documenting Waldenström's Macroglobulinemia to ensure proper reimbursement, maintain compliance, and reduce audit risk. These guidelines are particularly important when using ICD-10 code C88.00.

Impact

Clinical: May lead to inappropriate treatment., Regulatory: Non-compliance with coding guidelines., Financial: Potential for claim denials.

Mitigation Strategy

Ensure clinical documentation supports lab findings.

Impact

Reimbursement: Incorrect coding can lead to denied claims., Compliance: Non-compliance with coding standards., Data Quality: Inaccurate patient records and statistics.

Mitigation Strategy

Ensure documentation specifies WM with supporting lab results.

Impact

Inadequate documentation of diagnostic criteria.

Mitigation Strategy

Ensure all diagnostic criteria are documented in the patient's record.

Documentation errors, coding pitfalls, and audit risks are interconnected aspects of medical coding and billing. Addressing all three areas helps ensure accurate coding, optimal reimbursement, and regulatory compliance.

Frequently Asked Questions

Common questions about ICD-10 coding for Waldenström's Macroglobulinemia, with expert answers to help guide accurate code selection and documentation.

Documentation Templates for Waldenström's Macroglobulinemia

Use these documentation templates to ensure complete and accurate documentation for Waldenström's Macroglobulinemia. These templates include all required elements for proper coding and billing.

New Diagnosis

Specialty: Oncology

Required Elements

  • Patient history
  • Lab results
  • Bone marrow biopsy findings
  • Mutation analysis

Example Documentation

Patient presents with fatigue and blurred vision. Serum IgM 4.8 g/dL. Bone marrow biopsy confirms WM with 25% lymphoplasmacytic infiltration (CD19+/CD20+/CD5-). MYD88 L265P mutation detected.

Examples: Poor vs. Good Documentation

Poor Documentation Example
Patient has WM.
Good Documentation Example
Bone marrow aspirate shows 30% lymphoplasmacytic cells with CD19+/CD20+/CD5-/CD10- immunophenotype. Serum IgM 4.5 g/dL. MYD88 L265P mutation positive.
Explanation
The good example provides specific lab results and mutation confirmation, ensuring accurate diagnosis.

Need help with ICD-10 coding for Waldenström's Macroglobulinemia? Ask your questions below.

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