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ICD-10 Coding for Waldenström Macroglobulinemia(C88.0, C88.00, C88.01)

Complete ICD-10-CM coding and documentation guide for Waldenström Macroglobulinemia. Includes clinical validation requirements, documentation requirements, and coding pitfalls.

Also known as:

Lymphoplasmacytic LymphomaWM

Related ICD-10 Code Ranges

Complete code families applicable to Waldenström Macroglobulinemia

C88.0-C88.9Primary Range

Malignant immunoproliferative diseases

This range includes codes for Waldenström macroglobulinemia and related conditions.

Code Comparison: When to Use Each Code

Compare key differences between these codes to ensure accurate selection

CodeDescriptionWhen to UseKey Documentation
C88.0Waldenström macroglobulinemiaUse as a base code for WM diagnosis, specify remission status with C88.00 or C88.01.
  • Bone marrow biopsy showing ≥10% lymphoplasmacytic infiltration
  • Serum IgM monoclonal protein level
  • MYD88 L265P mutation
C88.00Waldenström macroglobulinemia not in remissionUse when WM is active and not in remission.
  • Hemoglobin <10 g/dL
  • Platelets <100k/µL
  • Constitutional symptoms
C88.01Waldenström macroglobulinemia in remissionUse when WM is in remission.
  • Bone marrow biopsy confirmation
  • IgM reduction by ≥50%

Clinical Decision Support

Always review the patient's clinical documentation thoroughly. When in doubt, choose the more specific code and ensure documentation supports it.

Key Information: ICD-10 code for Waldenström macroglobulinemia

Essential facts and insights about Waldenström Macroglobulinemia

The ICD-10 code for Waldenström macroglobulinemia is C88.0, with C88.00 for active disease and C88.01 for remission.

Primary ICD-10-CM Codes for waldenstrom macroglobulinemia

Waldenström macroglobulinemia
Non-billable Code

Decision Criteria

clinical Criteria

  • Presence of MYD88 L265P mutation

coding Criteria

  • Use C88.00 for active disease, C88.01 for remission

documentation Criteria

  • Document bone marrow biopsy and serum IgM levels

Applicable To

  • IgM monoclonal gammopathy
  • ≥10% bone marrow lymphoplasmacytic infiltration

Excludes

  • Small cell B-cell lymphoma (C83.0)
  • Multiple myeloma (C90.00)

Clinical Validation Requirements

  • Bone marrow biopsy showing ≥10% lymphoplasmacytic infiltration
  • Serum IgM monoclonal protein level
  • MYD88 L265P mutation

Code-Specific Risks

  • Incorrect use without specifying remission status
  • Confusion with other lymphomas

Coding Notes

  • Ensure remission status is documented and coded appropriately.

Ancillary Codes

Additional codes that should be used in conjunction with the main diagnosis codes when applicable.

Hyperviscosity syndrome

R68.2
Use if serum viscosity >5 cP or retinal hemorrhages are present.

IgM-related neuropathy

G62.81
Use for numbness/tingling in extremities with positive serum IgM.

Differential Codes

Alternative codes to consider when ruling out similar conditions to the primary diagnosis.

Small cell B-cell lymphoma

C83.0
Use if CD5+ or CD23+ on flow cytometry; WM is CD5-.

Multiple myeloma

C90.00
Exclude if lytic bone lesions are present; WM lacks osteolytic lesions.

Documentation & Coding Risks

Avoid these common documentation and coding issues when documenting Waldenström Macroglobulinemia to ensure proper reimbursement, maintain compliance, and reduce audit risk. These guidelines are particularly important when using ICD-10 code C88.0.

Impact

Clinical: Inaccurate treatment planning., Regulatory: Non-compliance with coding standards., Financial: Potential claim denials.

Mitigation Strategy

Verify remission status before coding.

Impact

Reimbursement: Incorrect coding can lead to denied claims., Compliance: Non-compliance with coding guidelines., Data Quality: Inaccurate patient records.

Mitigation Strategy

Always specify remission status with C88.00 or C88.01.

Impact

Failure to document remission status can lead to audit issues.

Mitigation Strategy

Implement checklist for remission documentation.

Documentation errors, coding pitfalls, and audit risks are interconnected aspects of medical coding and billing. Addressing all three areas helps ensure accurate coding, optimal reimbursement, and regulatory compliance.

Frequently Asked Questions

Common questions about ICD-10 coding for Waldenström Macroglobulinemia, with expert answers to help guide accurate code selection and documentation.

Documentation Templates for Waldenström Macroglobulinemia

Use these documentation templates to ensure complete and accurate documentation for Waldenström Macroglobulinemia. These templates include all required elements for proper coding and billing.

Oncology Progress Note

Specialty: Oncology

Required Elements

  • Assessment of WM status
  • Documentation of symptoms
  • Treatment plan

Example Documentation

**Assessment**: Waldenström macroglobulinemia (C88.00) with symptomatic hyperviscosity (R68.2). **Plan**: Plasmapheresis and ibrutinib therapy.

Examples: Poor vs. Good Documentation

Poor Documentation Example
Patient has WM.
Good Documentation Example
WM confirmed via bone marrow biopsy (30% lymphoplasmacytic cells, CD19+/CD20+/CD5-), serum IgM 4,200 mg/dL, MYD88 L265P mutation positive.
Explanation
The good example provides specific diagnostic criteria and lab results, supporting accurate coding.

Need help with ICD-10 coding for Waldenström Macroglobulinemia? Ask your questions below.

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