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Q82.2
Billable

Congenital cutaneous mastocytosis

Chapter 17: Congenital malformations, deformations and chromosomal abnormalities

Inclusion Terms

3 items
  • Congenital diffuse cutaneous mastocytosis
  • Congenital maculopapular cutaneous mastocytosis
  • Congenital urticaria pigmentosa

Excludes1

5 items
  • cutaneous mastocytosis NOS (D47.01)
  • diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01)
  • malignant mastocytosis (C96.2-)
  • systemic mastocytosis (D47.02)
  • urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01)

Billable Code

Q82.2 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.

Referenced in Diagnoses

Conditions that use this ICD-10 code in their documentation

Additional Information from Parent Codes

The following information may apply to this code from its parent codes in the ICD-10 hierarchy. This information is important for proper coding and classification.

Excludes1

4 items

From Q82:

  • acrodermatitis enteropathica (E83.2)
  • congenital erythropoietic porphyria (E80.0)
  • pilonidal cyst or sinus (L05.-)
  • Sturge-Weber (-Dimitri) syndrome (Q85.89)

Excludes2

1 item

From Q00-Q99:

  • inborn errors of metabolism (E70-E88)

Notes

1 item

From Q00-Q99:

  • Codes from this chapter are not for use on maternal records
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